All Stories

  1. ISHLT consensus statement: Perioperative management of patients with pulmonary hypertension and right heart failure undergoing surgery
  2. Cardiac Catheterization and Hemodynamics in a Multicenter Cohort of Children with Pulmonary Hypertension
  3. The Efficacy of a Commercial Physical Activity Monitor in Longitudinal Tracking of Pulmonary Hypertension Patients
  4. Lung transplantation disparities based on diagnosis for patients bridging to transplant on extracorporeal membrane oxygenation
  5. Characterisation of paediatric pulmonary hypertensive vascular disease from the PPHNet Registry
  6. Health disparities and treatment approaches in portopulmonary hypertension and idiopathic pulmonary arterial hypertension: an analysis of the Pulmonary Hypertension Association Registry
  7. Author rebuttal to response regarding “Letter to the Editor regarding ‘Could pulmonary arterial hypertension patients be at lower risk from severe COVID‐19?’”
  8. A rare childhood case of Behcet's disease and chronic thromboembolic pulmonary hypertension
  9. Care of patients with pulmonary arterial hypertension during the coronavirus (COVID‐19) pandemic
  10. Could pulmonary arterial hypertension patients be at a lower risk from severe COVID‐19?
  11. Response: Still puzzling about a clear definition of pulmonary arterial hypertension in newborns
  12. Sildenafil Use in Children with Pulmonary Hypertension
  13. Paediatric pulmonary arterial hypertension: updates on definition, classification, diagnostics and management
  14. Increasing Opportunity for Lung Transplant in Interstitial Lung Disease With Pulmonary Hypertension
  15. Eisenmenger Syndrome in Pregnancy
  16. Loss-of-Function ABCC8 Mutations in Pulmonary Arterial Hypertension
  17. Rare variants in SOX17 are associated with pulmonary arterial hypertension with congenital heart disease
  18. Challenges in Pulmonary Hypertension: Controversies in Treating the Tip of the Iceberg. A Joint National Institutes of Health Clinical Center and Pulmonary Hypertension Association Symposium Report
  19. The Left Ventricle in Congenital Diaphragmatic Hernia: Implications for the Management of Pulmonary Hypertension
  20. Position paper for the organization of ECMO programs for cardiac failure in adults
  21. Eisenmenger Syndrome and Pregnancy
  22. Update on pulmonary arterial hypertension research: proceedings from a meeting of experts
  23. Mutations in BMPR2 are not present in patients with pulmonary hypertension associated with congenital diaphragmatic hernia
  24. PVDOMICS
  25. A Computable Phenotype Improves Cohort Ascertainment in a Pediatric Pulmonary Hypertension Registry
  26. Evaluation and Management of Pulmonary Hypertension in Children with Bronchopulmonary Dysplasia
  27. Portopulmonary hypertension in children: a rare but potentially lethal and under-recognized disease
  28. Novel Modified Potts shunt design for Pulmonary Hypertension
  29. The “Central Sport Model”
  30. Characterization of a caveolin-1 mutation associated with both pulmonary arterial hypertension and congenital generalized lipodystrophy
  31. Corrigendum to “FUTURE-2: Results from an open-label, long-term safety and tolerability extension study using the pediatric FormUlation of bosenTan in pUlmonary arterial hypeRtEnsion” [Int. J. Cardiol. 202 (2016) 52–58]
  32. Right ventricular assist device use in ventricular failure due to pulmonary arterial hypertension: Lessons learned
  33. Chronic Thromboembolic Pulmonary Hypertension, Pregnancy, and a Pulmonary Endarterectomy: A Rare Challenge
  34. Clinical Classification in Pediatric Pulmonary Arterial Hypertension Associated with Congenital Heart Disease
  35. An Observational Study of Inhaled-Treprostinil Respiratory-Related Safety in Patients with Pulmonary Arterial Hypertension
  36. Extracorporeal Membrane Oxygenation for Cardiopulmonary Failure During Pregnancy and Postpartum
  37. Growth in children with pulmonary arterial hypertension: a longitudinal retrospective multiregistry study
  38. Recommendations for the Use of Inhaled Nitric Oxide Therapy in Premature Newborns with Severe Pulmonary Hypertension
  39. Using Registries to Understand Clinical Practice
  40. BMPR2 mutations and survival in pulmonary arterial hypertension: an individual participant data meta-analysis
  41. Therapeutic Options for Childhood Pulmonary Hypertension
  42. PH Roundtable: Pediatric Pulmonary Hypertension Guidelines Highlights and Challenges
  43. FUTURE-2: Results from an open-label, long-term safety and tolerability extension study using the pediatric FormUlation of bosenTan in pUlmonary arterial hypeRtEnsion
  44. Predicting Peak Oxygen Uptake From the 6-Minute Walk Test in Patients With Pulmonary Hypertension
  45. Pediatric Pulmonary Hypertension
  46. Pulmonary hypertension in chronic lung disease of infancy
  47. Balloon atrial septostomy in pulmonary arterial hypertension: Effect on survival and associated outcomes
  48. Challenges and Current Efforts in the Development of Biomarkers for Chronic Inflammatory and Remodeling Conditions of the Lungs
  49. Pharmacologic Therapy for Pulmonary Arterial Hypertension in Adults
  50. Risk Factors for Death in 632 Patients with Sickle Cell Disease in the United States and United Kingdom
  51. Subcutaneous Treprostinil for Pulmonary Hypertension in Chronic Lung Disease of Infancy
  52. Survival Differences in Pediatric Pulmonary Arterial Hypertension
  53. An Official American Thoracic Society Clinical Practice Guideline: Diagnosis, Risk Stratification, and Management of Pulmonary Hypertension of Sickle Cell Disease
  54. Effects of Dose and Age on Adverse Events Associated with Tadalafil in the Treatment of Pulmonary Arterial Hypertension
  55. EIF2AK4 Mutations in Pulmonary Capillary Hemangiomatosis
  56. Extracorporeal Membrane Oxygenation With Subclavian Artery Cannulation in Awake Patients With Pulmonary Hypertension
  57. Extracorporeal Membrane Oxygenation as a Novel Bridging Strategy for Acute Right Heart Failure in Group 1 Pulmonary Arterial Hypertension
  58. Four- and Seven-Year Outcomes of Patients With Congenital Heart Disease–Associated Pulmonary Arterial Hypertension (from the REVEAL Registry)
  59. Pediatric Pulmonary Hypertension
  60. Pulmonary Arterial Hypertension Associated with Congenital Heart Disease
  61. Safety of Cardiac Catheterization at a Center Specializing in the Care of Patients with Pulmonary Arterial Hypertension
  62. A Novel Channelopathy in Pulmonary Arterial Hypertension
  63. Outcomes of Congenital Diaphragmatic Hernia in the Modern Era of Management
  64. Upper-Body Extracorporeal Membrane Oxygenation as a Strategy in Decompensated Pulmonary Arterial Hypertension
  65. Genome-wide association analysis identifies a susceptibility locus for pulmonary arterial hypertension
  66. Implications of the U.S. Food and Drug Administration Warning against the Use of Sildenafil for the Treatment of Pediatric Pulmonary Hypertension
  67. Genetic determinants of haemolysis in sickle cell anaemia
  68. Rapid Transition from Inhaled Iloprost to Inhaled Treprostinil in Patients with Pulmonary Arterial Hypertension
  69. Clinical Trials in Neonates and Children: Report of the Pulmonary Hypertension Academic Research Consortium Pediatric Advisory Committee
  70. Treatment satisfaction is associated with improved quality of life in patients treated with inhaled treprostinil for pulmonary arterial hypertension
  71. Updating Clinical Endpoint Definitions
  72. Effectiveness and Safety of Inhaled Treprostinil for the Treatment of Pulmonary Arterial Hypertension in Children
  73. Safety and Efficacy of Transition from Systemic Prostanoids to Inhaled Treprostinil in Pulmonary Arterial Hypertension
  74. The relationship between the severity of hemolysis, clinical manifestations and risk of death in 415 patients with sickle cell anemia in the US and Europe
  75. Congenital heart disease and pulmonary hypertension: pharmacology and feasibility of late surgery
  76. Successful Treatment of Severe Mechanical Mitral Valve Thrombosis With Tissue Plasminogen Activator in a 7-Month-Old Infant
  77. Pediatric Pulmonary Arterial Hypertension and Hyperthyroidism: A Potentially Fatal Combination
  78. Whole Exome Sequencing to Identify a Novel Gene (Caveolin-1) Associated With Human Pulmonary Arterial Hypertension
  79. Clinical safety, pharmacokinetics, and efficacy of ambrisentan therapy in children with pulmonary arterial hypertension
  80. Echocardiographic Markers of Elevated Pulmonary Pressure and Left Ventricular Diastolic Dysfunction Are Associated With Exercise Intolerance in Adults and Adolescents With Homozygous Sickle Cell Anemia in the United States and United Kingdom
  81. Hospitalization for pain in patients with sickle cell disease treated with sildenafil for elevated TRV and low exercise capacity
  82. Randomized Clinical Trial of Aspirin and Simvastatin for Pulmonary Arterial Hypertension: ASA-STAT
  83. Ambrisentan for Pulmonary Arterial Hypertension Due to Congenital Heart Disease
  84. Pulmonary hypertension in children with sickle cell disease
  85. Common Atrium and Pulmonary Vascular Disease
  86. Two Cases of Pulmonary Hypertension Associated with Type III Glycogen Storage Disease
  87. Long-Term Outcomes in Children With Pulmonary Arterial Hypertension Treated With Bosentan in Real-World Clinical Settings
  88. Effectiveness of Transition from Intravenous Epoprostenol to Oral/Inhaled Targeted Pulmonary Arterial Hypertension Therapy in Pediatric Idiopathic and Familial Pulmonary Arterial Hypertension
  89. Tadalafil for the treatment of pulmonary arterial hypertension
  90. Non-congenital heart disease associated pediatric pulmonary arterial hypertension
  91. Pulmonary arterial hypertension in children: Diagnostic work-up and challenges
  92. Doppler-defined pulmonary hypertension and the risk of death in children with sickle cell disease followed for a mean of three years
  93. Polymorphism in the Angiotensin II Type 1 Receptor (AGTR1) is Associated With Age at Diagnosis in Pulmonary Arterial Hypertension
  94. Determinants of Right Ventricular Ejection Fraction in Pulmonary Arterial Hypertension
  95. Pulmonary arterial hypertension in children: A Medical Update
  96. Clinical Implications of Determining BMPR2 Mutation Status in a Large Cohort of Children and Adults With Pulmonary Arterial Hypertension
  97. Pulmonary arterial hypertension in children: a medical update
  98. Plasma serotonin levels are normal in pulmonary arterial hypertension
  99. Pulmonary artery hypertension in a child with MELAS due to a point mutation of the mitochondrial tRNA(Leu) gene (m.3243A>G)
  100. The effect of atrial septostomy on the concentration of brain-type natriuretic peptide in patients with idiopathic pulmonary arterial hypertension
  101. Platelet-Derived Growth Factor Is Increased in Pulmonary Capillary Hemangiomatosis
  102. Emerging treatments for pulmonary arterial hypertension
  103. Selective serotonin reuptake inhibitor use and outcomes in pulmonary arterial hypertension
  104. Reply
  105. Pulmonary Arterial Hypertension
  106. A SECONDARY CARE PERSPECTIVE ON THE STEPPING-DOWN OF INHALED CORTICOSTEROID THERAPY IN PATIENTS WITH STABLE ASTHMA
  107. von Willebrand Factor Independently Predicts Long-term Survival in Patients With Pulmonary Arterial Hypertension
  108. Effects of Long-Term Bosentan in Children With Pulmonary Arterial Hypertension
  109. Idiopathic pulmonary arterial hypertension in children
  110. New predictors of outcome in idiopathic pulmonary arterial hypertension
  111. Outcomes in Children With Idiopathic Pulmonary Arterial Hypertension
  112. Identical Twins With Primary Pulmonary Hypertension
  113. Pulmonary arterial hypertension in children
  114. Pulmonary hypertension in Jarcho-Levin syndrome
  115. Eisenmenger syndrome in ventricular septal defect patients
  116. Novel therapeutics for the treatment of paediatric pulmonary arterial hypertension
  117. Long-Term Prostacyclin for Pulmonary Hypertension With Associated Congenital Heart Defects
  118. Late Left Ventricular Function After Surgery for Children With Chronic Symptomatic Mitral Regurgitation