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  1. Serum phospholipid fatty acids are associated with bone mass in healthy 4-years-old children.
  2. Elevated plasma phospholipid n-3 docosapentaenoic acid concentrations during hibernation
  3. The fatty acid imbalance of cystic fibrosis exists at birth independent of feeding in pig and ferret models
  4. Geographical distribution of cystic fibrosis carriers as population genetic determinant of COVID-19 spread and fatality in 37 countries
  5. Omega-3 fatty acids decrease CRYAB, production of oncogenic prostaglandin E2 and suppress tumor growth in medulloblastoma
  6. Ursodeoxycholic acid and liver disease associated with cystic fibrosis: A multicenter cohort study
  7. Nutrition in Cystic Fibrosis—Some Notes on the Fat Recommendations
  8. Liver X receptor β regulates bile volume and the expression of aquaporins and cystic fibrosis transmembrane conductance regulator in the gallbladder
  9. Body surface area-based omega-3 fatty acids supplementation strongly correlates to blood concentrations in children.
  10. Is the ENaC Dysregulation in CF an Effect of Protein-Lipid Interaction in the Membranes?
  11. P059 A double-blind randomised multi-centre European study of linoleic acid supplementation for one year in patients with cystic fibrosis
  12. Abnormal n-6 fatty acid metabolism in cystic fibrosis contributes to pulmonary symptoms
  13. Chapter 2. ESPGHAN: 50 Years Memories—The Early Years
  14. Chapter 8. 50 Years of the European Society for Paediatric Gastroenterology, Hepatology and Nutrition (ESPGHAN): Captivating Witness Reports of a Success Story
  15. Low linoleic and high docosahexaenoic acids in a severe phenotype of transgenic cystic fibrosis mice
  16. Serum n-6 and n-9 Fatty Acids Correlate With Serum IGF-1 and Growth Up to 4 Months of Age in Healthy Infants
  17. 304 Severe phenotype of CF mice with low linoleic acid and high docosahexaenoic acid concentrations in serum phospholipids
  18. Highlights of the ESPEN-ESPGHAN-ECFS Guidelines on Nutrition Care for Infants and Children With Cystic Fibrosis
  19. ESPEN-ESPGHAN-ECFS guidelines on nutrition care for infants, children, and adults with cystic fibrosis
  20. Long-chain saturated and monounsaturated fatty acids associate with development of premature infants up to 18 months of age
  21. Antinociceptive fatty acid patterns differ in children with psychosomatic recurrent abdominal pain and healthy controls
  22. The development of infants born to obese mothers might be related to omega-3 fatty acid status
  23. Perinatal programming by diets with essential fatty acid deficient/high saturated fatty acids or different n-6/n-3 ratios for diseases in adulthood
  24. Lipid Quality in Infant Nutrition
  25. Can Lipidomics Conceal the Key for Understanding Celiac Disease?
  26. Dietary Fat and Fat Metabolism in CF
  27. Essential Fatty Acid Deficiency in Cystic Fibrosis
  28. IL-1β expression in the distal lung epithelium disrupts lung morphogenesis and epithelial cell differentiation in fetal mice
  29. Omega-6 and omega-3 fatty acids in milk and beneficial impact on the infant
  30. Nervonic acid is much lower in donor milk than in milk from mothers delivering premature infants—Of neglected importance?
  31. Polyamine levels in breast milk are associated with mothers' dietary intake and are higher in preterm than full-term human milk and formulas
  32. Lower polyamine levels in breast milk of obese mothers compared to mothers with normal body weight
  33. Different fatty acid pattern in breast milk of obese compared to normal-weight mothers
  34. Relation Between Dietary Fat Intake Type and Serum Fatty Acid Status in Children With Cystic Fibrosis
  35. 243 IMPACT OF CHILDHOOD SOCIOECONOMIC STATUS ON SERUM LEVEL OF OMEGA-3 FATTY ACIDS AND CARDIOVASCULAR RISK FACTORS IN HEALTHY ADOLESCENTS. A 3-YEAR FOLLOW-UP STUDY
  36. Reasons given by mothers for discontinuing breastfeeding in Iran
  37. Motor, mental and behavioral developments in infancy are associated with fatty acid pattern in breast milk and plasma of premature infants
  38. High Physiological Omega-3 Fatty Acid Supplementation Affects Muscle Fatty Acid Composition and Glucose and Insulin Homeostasis in Obese Adolescents
  39. Response to the letter by Ooi et al.
  40. The omega-6/omega-3 ratio is of importance!
  41. Early behavior and development are influenced by the n-6 and n-3 status in prematures
  42. Postnatal essential fatty acid deficiency in mice affects lipoproteins, hepatic lipids, fatty acids and mRNA expression
  43. Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease
  44. New clinical diagnostic procedures for cystic fibrosis in Europe
  45. Prenatal essential fatty acid deficiency in mice results in long-term gender-specific effects on body weight and glucose metabolism
  46. Noncirrhotic presinusoidal portal hypertension is common in cystic fibrosis-associated liver disease
  47. Postnatal deficiency of essential fatty acids in mice results in resistance to diet-induced obesity and low plasma insulin during adulthood
  48. The skinny on tuna fat: health implications
  49. From the Swedish to the Mediterranean Diet and the Omega-6/Omega-3 Balance
  50. Optimal vitamin A and suboptimal vitamin D status are common in Iranian infants
  51. Omega-3 fatty acid supplementation improves vascular function and reduces inflammation in obese adolescents
  52. Inverse relation between vitamin D and serum total immunoglobulin G in the Scandinavian Cystic Fibrosis Nutritional Study
  53. Fatty acid metabolism in cystic fibrosis
  54. High levels of soluble intercellular adhesion molecule-1, insulin resistance and saturated fatty acids are associated with endothelial dysfunction in healthy adolescents
  55. Early behaviour and development in breast-fed premature infants are influenced by omega-6 and omega-3 fatty acid status
  56. Food choice is reflected in serum markers and anthropometric measures in healthy 8-yr-olds
  57. EPA supplementation improves teacher-rated behaviour and oppositional symptoms in children with ADHD
  58. Supplementation With Fatty Acids Influences the Airway Nitric Oxide and Inflammatory Markers in Patients With Cystic Fibrosis
  59. Fatty acid composition of diet, cord blood and breast milk in Chinese mothers with different dietary habits
  60. Metabolic profiles of fat and glucose differ by gender in healthy 8-year-olds
  61. Heart rate recovery in young adult patients with cystic fibrosis
  62. Processed animal products with emphasis on polyunsaturated fatty acid content
  63. Ezrin-Radixin-Moesin-Binding Phosphoprotein (EBP50), an Estrogen-Inducible Scaffold Protein, Contributes to Biliary Epithelial Cell Proliferation
  64. Fatty acid pattern in serum is associated with bone mineralisation in healthy 8-year-old children
  65. Breastfeeding in Iran: prevalence, duration and current recommendations
  66. Fatty acid patterns early after premature birth, simultaneously analysed in mothers' food, breast milk and serum phospholipids of mothers and infants
  67. Liver function and morphology during long-term fatty acid supplementation in cystic fibrosis
  68. Liver damage in juvenile inflammatory bowel disease
  69. Serum Linoleic Acid Status as a Clinical Indicator of Essential Fatty Acid Status in Children With Cystic Fibrosis
  70. Volumetric bone mineral density is an important tool when interpreting bone mineralization in healthy children
  71. SUPPLEMENT WITH OMEGA 3 FATTY ACIDS IMPROVES ENDOTHELIAL FUNCTION IN OBESE ADOLESCENTS
  72. Is the relatively low intake of omega‐3 fatty acids in Western diet contributing to the obesity epidemics?
  73. Muscular strength after different types of training in physically active patients with cystic fibrosis
  74. Cardiopulmonary Data in Response to 6 Months of Training in Physically Active Adult Patients with Classic Cystic Fibrosis
  75. Fatty acid composition in breast milk and serum phospholipids of healthy term Chinese infants during first 6 weeks of life
  76. Abstract 3646: Supplement with Omega-3 Fatty Acids Lowers Pulse Wave Velocity in Obese Adolescents
  77. Dornase alfa is well tolerated: Data from the Epidemiologic Registry of Cystic Fibrosis
  78. Docosahexaenoic acid is associated with endosteal circumference in long bones in young males with cystic fibrosis
  79. 235 Serum vitamin E and IL-6 are influenced by type of physical training in patients with CF
  80. Airway Nitric Oxide in Patients With Cystic Fibrosis Is Associated With Pancreatic Function, Pseudomonas Infection, and Polyunsaturated Fatty Acids
  81. Food choice, socio-economic characteristics and health in 4-year olds in a well-educated urban Swedish community
  82. Swedish pre-school children eat too much junk food and sucrose
  83. Ultraviolet B radiation improves serum levels of vitamin D in patients with cystic fibrosis
  84. Epithelial Electrical Resistance as a Measure of Permeability Changes in Pediatric Duodenal Biopsies
  85. Metabolic markers in relation to nutrition and growth in healthy 4-y-old children in Sweden
  86. Serum Phospholipid Fatty Acids, Adipose Tissue, and Metabolic Markers in Obese Adolescents*
  87. LINOLEIC ACID STATUS FOR THE DIAGNOSIS OF ESSENTIAL FATTY ACID DEFICIENCY IN CHILDREN WITH CYSTIC FIBROSIS
  88. Abnormal Fatty Acid Pattern in Intestinal Mucosa of Children With Celiac Disease Is Not Reflected in Serum Phospholipids
  89. Mediterranean diet and cystic fibrosis
  90. Serum phospholipid fatty acid pattern is associated with bone mineral density in children, but not adults, with cystic fibrosis
  91. 312 EBP50, a scaffold protein participating in the proliferation of cholangiocytes, is delocalized in the ductular reaction associated with cystic fibrosis liver disease
  92. Mediterranean-inspired diet lowers the ratio of serum phospholipid n–6 to n–3 fatty acids, the number of leukocytes and platelets, and vascular endothelial growth factor in healthy subjects
  93. Die Versorgung von Mukoviszidose-Patienten
  94. Care of Patients with Cystic Fibrosis
  95. Perinatal PUFA Intake Affects Leptin and Oral Tolerance in Neonatal Rats and Possibly Immunoreactivity in Intrauterine Growth Retardation in Man
  96. 212 Working capacity and lung function in physically active patients with Cystic Fibrosis were unchanged after 6 months of training
  97. 280 Serum phospholipid fatty acid pattern is associated with bone growth in children but not adults with Cystic Fibrosis
  98. Asistencia de pacientes con fibrosis quística
  99. Soins des patients atteints d’une mucoviscidose
  100. Trampolines are Useful in the Treatment of Cystic Fibrosis Patients
  101. ESSENTIAL FATTY ACID DEFICIENCY AND THE CLINICAL RELEVANCE OF THE TRIENE:TETRAENE RATIO IN CHILDREN WITH CYSTIC FIBROSIS
  102. Muscular Strength and Function in Patients With Cystic Fibrosis
  103. Cost-Effectiveness of Alendronate in the Prevention of Osteoporotic Fractures in Danish Women
  104. DISTURBED PHOSPHOLIPID FATTY ACID PATTERN IN INTESTINAL BIOPSIES FROM PATIENTS WITH COELIAC DISEASE
  105. MARKED CHANGES IN THE MRNA EXPRESSION OF PPARS IN THE LIVER OF MICE WITH PERINATAL ESSENTIAL FATTY ACID DEFICIENCY
  106. Gender-related long-term effects in adult rats by perinatal dietary ratio of n-6/n-3 fatty acids
  107. Cysteinyl leukotrienes are secretagogues in atrophic coeliac and in normal duodenal mucosa of children
  108. Perinatal essential fatty acid deficiency influences body weight and bone parameters in adult male rats
  109. Dietary n-6:n-3 fatty acid ratio in the perinatal period affects bone parameters in adult female rats
  110. The ratio of n-6 to n-3 fatty acids in maternal diet influences the induction of neonatal immunological tolerance to ovalbumin
  111. Normal Annual Increase of Bone Mineral Density During Two Years in Patients With Cystic Fibrosis
  112. Modulation of neonatal immunological tolerance to ovalbumin by maternal essential fatty acid intake
  113. Duodenogastric Bile Reflux Is Common in Cystic Fibrosis
  114. Severe Hypercholesterolaemia Leads to Strong Th2 Responses to an Exogenous Antigen
  115. Fatty Acid Metabolism in Cystic Fibrosis
  116. Association between serum oncofetal antigens CA 19-9 and CA 125 and clinical status in patients with cystic fibrosis
  117. Dornase alfa in the treatment of cystic fibrosis in Europe: A report from the Epidemiologic Registry of Cystic Fibrosis
  118. The Transfer of Immunity from Mother to Child
  119. Decreased bone mineral density in normal-growing patients with cystic fibrosis
  120. Leptin levels in rat offspring are modified by the ratio of linoleic to α-linolenic acid in the maternal diet
  121. Breast-feeding, a complex support system for the offspring
  122. Breast‐feeding, a complex support system for the offspring
  123. Maternal Dietary Intake of Essential Fatty Acids Affects Adipose Tissue Growth and Leptin mRNA Expression in Suckling Rat Pups
  124. Predictors of deterioration of lung function in cystic fibrosis*
  125. Electrogenic Ion Transport in Duodenal Biopsies from Children with Coeliac Disease
  126. Essential fatty acid deficiency in relation to genotype in patients with cystic fibrosis
  127. Presence of cystic fibrosis‐related diabetes mellitus is tightly linked to poor lung function in patients with cystic fibrosis: Data from the European Epidemiologic Registry of Cystic Fibrosis
  128. Water-miscible tocopherol is not superior to fat-soluble preparation for vitamin E absorption in cystic fibrosis
  129. Spectrum of Mutations in theCFTRGene of Patients with Classical and Atypical Forms of Cystic Fibrosis from Southwestern Sweden: Identification of 12 Novel Mutations
  130. Factors associated with poor pulmonary function: cross-sectional analysis of data from the ERCF
  131. Gastric IgA in Cystic Fibrosis in Relation to the Migrating Motor Complex
  132. Allergic bronchopulmonary aspergillosis in cystic fibrosis
  133. Maternal essential fatty acid deficiency depresses serum leptin levels in suckling rat pups
  134. Gastric Secretion in Cystic Fibrosis in Relation to the Migrating Motor Complex
  135. European Epidemiologic Registry of Cystic Fibrosis (ERCF): Comparison of major disease manifestations between patients with different classes of mutations
  136. Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study
  137. Essential fatty acid deficiency affects the fatty acid composition of the rat small intestinal and colonic mucosa differently
  138. Diagnostic test meal in childhood enteropathy using simultaneous carbohydrate and fat loading
  139. Expression of cystic fibrosis transmembrane conductance regulator in liver tissue from patients with cystic fibrosis
  140. Characterization of a novel 21-kb deletion, CFTRdele2,3(21 kb), in the CFTR gene: a cystic fibrosis mutation of Slavic origin common in Central and East Europe
  141. Electrogenic Ion Transport in Duodenum, an Aid in Cystic Fibrosis Diagnosis
  142. Nutritional management in cystic fibrosis
  143. Natural history of liver disease in cystic fibrosis
  144. Composition and permeability of syncytiotrophoblast plasma membranes in pregnancies complicated by intrauterine growth restriction
  145. Allergy to laboratory animals in children of parents occupationally exposed to mice, rats and hamsters
  146. Therapeutic drug monitoring in patients with cystic fibrosis and mycobacterial disease
  147. 17. Eight new mutations identified at the West Swedish CF-center
  148. 65. Totally implantable venous access in patients with cystic fibrosis (CF)
  149. E2.1 Risk factors of importance for long-term survival of patients with cystic fibrosis
  150. E2.3 The European Epidemiological Registry of Cystic Fibrosis (ERCF). Does pulmozyme make any difference?
  151. CHLORIDE SECRETION IN DUODENUM, AN AID IN CYSTIC FIBROSIS (CF) DIAGNOSIS
  152. BILE ACID REGURGITATION INTO THE STOMACH IS A COMMON FINDING IN CYSTIC FIBROSIS (CF)
  153. GASTRIC IgA IN CYSTIC FIBROSIS (CF) IN RELATION TO MIGRATING MOTOR COMPLEXES (MMC)
  154. Multicenter, open-label study of recombinant human DNase in cystic fibrosis patients with moderate lung disease
  155. RAT SERUM ARCHIDONIC ACID DECLINES DURING THE LACTATION PERIOD
  156. ESSENTIAL FATTY ACID DEFICIENCY DIFFERENTLY AFFECTS THE FATTY ACID COMPOSITION OF THE RAT INTESTINAL AND COLONIC MUCOSA.
  157. PROSPECTIVE STUDY OF LIVER DISEASE FOR 15 YEARS IN CYSTIC FIBROSIS (CF)
  158. URINARY BILE ACID EXCTRETION PATTERN IN CHILDREN WITH AAGENAES SYNDROME
  159. A two-year prospective study of the effect of ursodeoxycholic acid on urinary bile acid excretion and liver morphology in cystic fibrosis-associated liver disease
  160. Intestinal Permeability in Cystic Fibrosis in Relation to Genotype
  161. Reply to Angelico
  162. EFFECTS OF ARACHIDONIC ACID METABOLITES ON RECTAL ION TRANSPORT IN ULCERATIVE COLITIS
  163. Vitamin A Concentration in the Liver Decreases with Age in Patients with Cystic Fibrosis
  164. Electrogenic Ion Transport along the Human Duodenum in Childhood
  165. Prostanoid biosynthesis in patients with cystic fibrosis
  166. Bile acid kinetics and biliary lipid composition in cystic fibrosis
  167. Cystic Fibrosis Pulmonary Infection: The Swedish Experience
  168. Metabolism of orally fed [3H]-eicosapentaenoic and [14C]-arachidonic acid in essential fatty acid-deficient rats
  169. Leukotriene B4 and C4 Metabolism in Small Intestine Mucosa of Children with Celiac Disease
  170. Leukotriene B4and C4generation by human leukocytes after ex vivo stimulation with Ca-ionophore and opsonized zymosan in children with atopic asthma
  171. 51 INTESTINAL PERMEABILITY IN CYSTIC FIBROSIS (CF) IN RELATION TO GENOTYPE AND ESSENTIAL FATTY ACID DEFICIENCY (EFAD)
  172. 52 ESSENTIAL FATTY ACID DEFICIENCY (EFAD) IN RELATION TO GENOTYPE IN CYSTIC FIBROSIS (CF)
  173. Incidence of liver disease in patients with cystic fibrosis and meconium ileus
  174. Defective inhibition by dexamethasone of leukotriene B4 and C4 production by leukocytes in patients with cystic fibrosis
  175. 73 ELECTROGENIC ION TRANSPORT IN HUMAN DUODENUM
  176. 74 EFFECTS OF LEUKOTRIENES ON ION TRANSPORT IN HUMAN DUODENUM
  177. Inhibitory effects of theophylline, terbutaline, and hydrocortisone on leukotriene B4 and C4 generation by human leukocytes in vitro
  178. Bacterial colonisation withXanthomonas maltophilia — A retrospective study in a cystic fibrosis patient population
  179. Leukotriene B4and C4generation by blood leukocytes after ex vivo stimulation by Ca-ionophore and opsonized zymosan in children with atopic dermatitis
  180. Bile salt sulphotransferase activity in the liver of cholestatic infants
  181. High doses of aminoglycosides did not produce liver toxicity in patients with cystic fibrosis
  182. The urinary bile acid excretion in healthy premature and full-term infants during the neonatal period
  183. Effects of Different Formula Feeds on the Developmental Pattern of Urinary Bile Acid Excretion in Infants
  184. Effects of Pancreatic and Snake Venom Phospholipase A2 on the Generation of Leukotriene B4 and C4 by Human Leukocytes in Vitro
  185. Cystic Fibrosis Is Treatment with Ursodeoxycholic Acid of Value?
  186. Leukotriene B<sub>4</sub> and C<sub>4</sub> Generation by Small Intestinal Mucosa in Children with Coeliac Disease
  187. Leukotriene B4 generation by blood polymorphonuclear leukocytes after incubation in urine
  188. Immunoglobulin G antibodies toPseudomonas aeruginosa lipopolysaccharides and exotoxin A in patients with cystic fibrosis or bacteremia
  189. Frequency of four cystic fibrosis mutations in a Swedish population
  190. Nephrolithiasis in cystic fibrosis
  191. Leukotriene B4 and C4 Generation by Human Colostral Macrophages in vitro
  192. Increased oral bioavailability of ciprofloxacin in cystic fibrosis patients.
  193. Capacity of Small Intestinal Mucosa to Produce Leukotriene B4 and C4 in Children with Celiac Disease
  194. 6 ACCUMULATION OF IRON IN LIVERS FROM RATS DEFICIENT IN ESSENTIAL FATTY ACIDS (EFA);
  195. 73 LEUKOTRIENE B4 and C4 GENERATION IN SMALL INTESTINAL MUCOSA OF CHILDREN WITH COELIAC DISEASE
  196. Incorporation of dietary [14C]arachidonic acid and [3H]eicosapentaenoic acid into tissue lipids during absorption of a fish oil emulsion.
  197. Bile-duct destruction and collagen deposition: A prominent ultrastructural feature of the liver in cystic fibrosis
  198. The effect of essential fatty acid deficiency on hepatic bile salt sulphotransferase in rats
  199. Erythrocyte Sodium-Potassium Transport in Cystic Fibrosis
  200. Serum Primary Bile Acids in the Course of Celiac Disease in Children
  201. Craniofacial morphology in children with cystic fibrosis
  202. Home intravenous antibiotic treatment of patients with cystic fibrosis
  203. Long-term double-blind study on the influence of dietary fibres on faecal bile acid excretion in juvenile ulcerative colitis
  204. Liver Transplantation in a Boy with Acute Porphyria Due to Aminolaevulinate Dehydratase Deficiency
  205. The fertility potential of male cystic fibrosis patients
  206. Faecal bile acid excretion in children with inflammatory bowel disease.
  207. ABSORPTION AND METABOLISM OF 3H-EICOSAPENTAENOIC (EPA) AND 14C-ARACHIDONIC (AA) ACIDS IN NORMAL AND ESSENTIAL FATTY ACID (EFA) DEFICIENT RATS
  208. A simplified analysis of fatty acids in serum phospholipids using Sep-Pak cartridges
  209. Decreased Renal Clearance of Sodium in Cystic Fibrosis
  210. Serum Bile Acids in Relation to Disease Activity and Intake of Dietary Fibers in Juvenile Ulcerative Colitis
  211. Adaptive regulation of lipoprotein lipase and salt-resistant lipase activities in essential fatty acid deficiency: An experimental study in the rat
  212. Renal Function in Rats with Essential Fatty Acid Deficiency
  213. Pancreatic function in the essential fatty acid deficient rat
  214. Absorption and metabolism of [3H]arachidonic and [14C]linoleic acid in essential fatty acid-deficient rats
  215. Passive smoking in cystic fibrosis
  216. Metabolism of [3H]arachidonic acid- and [14C]linoleic acid-labelled chylomicrons in essential fatty acid-deficient rats
  217. Prospective study of mycobacterial infections in patients with cystic fibrosis.
  218. Antistaphylococcal antibodies in cystic fibrosis
  219. Phenobarbital Can Aggravate a Cholestatic Bile Acid Pattern in Infants with Obstructive Cholangiopathy
  220. Increased Renal Clearance of Cefsulodin Due to Higher Glomerular Filtration Rate in Cystic Fibrosis
  221. Ketonic bile acids in urine of infants during the neonatal period.
  222. Relation between Essential Fatty Acid Metabolism and Gastrointestinal Symptoms in Cystic Fibrosis
  223. PANCREATIC FUNCTION IN ESSENTIAL FATTY ACID DEFICIENT (EFAD) RATS
  224. Effect on renal function of essential fatty acid supplementation in cystic fibrosis
  225. Na, K-ATPase Activity in Rectal Mucosa of Children with Ulcerative Colitis and Crohn's Disease
  226. Serum and sputum concentrations of netilmicin in combination with acylureidopenicillin and cephalosporins in clinical treatment of pulmonary exacerbations in cystic fibrosis
  227. Increased bronchial chloride concentration in cystic fibrosis
  228. Increased nonrenal clearance and increased diuretic efficiency of furosemide in cystic fibrosis
  229. 93 FECAL BILE ACID (BA) EXCRETION IN CHILDREN WITH INFLAMMATORYDISEASE (IBD)
  230. 96 ABSORPTION AND LIVER UPTAKE OF 3H-ARACHIDONIC ACID AND C-LINOLEIC ACID IN ESSENTIAL FATTY ACID DEFICIENT (EFAD) RATS
  231. 95 ARACHIDONIC ACID RELEASE AND ESSENTIAL FATTY ACID DEFICIENCY IN CYSTIC FIBROSIS
  232. 77 PHENOBARBITAL (P) INCREASES CHOLESTASIS IN LIVER DISEASE – A HAZARD TO INFANTS?
  233. Discussion
  234. Composition and surface properties of the bronchial lipids in adult patients with cystic fibrosis
  235. DEFECTIVE BILE ACID AMIDATION: PREDICTED FEATURES OF A NEW INBORN ERROR OF METABOLISM
  236. Antibiotic Therapy of Pulmonary Infections in Cystic Fibrosis
  237. Antibiotic therapy of pulmonary infections in cystic fibrosis. Dosage schedules and duration of treatment
  238. Influence of the Glomerular Filtration Rate on Renal Clearance of Ceftazidime in Cystic Fibrosis
  239. 3-OXO-Δ4 BILE ACIDS IN LIVER DISEASE
  240. HAEMORRHAGIC PANCREATITIS AFTER ERCP IN PATIENTS WITH ALPHA1-ANTITRYPSIN DEFICIENCY
  241. Reply
  242. Imipenem/cilastatin, an alternative treatment of pseudomonas infection in cystic fibrosis
  243. Food Intake in Patients with Cystic Fibrosis on an Ordinary Diet
  244. Home Intravenous Antibiotic Treatment in Cystic Fibrosis
  245. Relation between Defective Regulation of Arachidonic Acid Release and Symptoms in Cystic Fibrosis
  246. Sclerosing Cholangitis in Cystic Fibrosis
  247. Prospective study of serum antibodies to Pseudomonas aeruginosa exoproteins in cystic fibrosis
  248. Prospective study of serum staphylococcal antibodies in cystic fibrosis.
  249. Granulocyte elastase-α1-antiproteinase complex in cystic fibrosis: Sensitive plasma assay for monitoring pulmonary infections
  250. Relation between clinical and roentgenological scores and measures of lung function in cystic fibrosis, with special reference to pulmonary Xenon133 elimination
  251. 2. SCLEROSING CHOLANGITIS IN CYSTIC FIBROSIS
  252. Psychosocial Stressors and Gastrointestinal Disorders in Childhood and Adolescense
  253. Pathological regulation of arachidonic acid release in cystic fibrosis: the putative basic defect.
  254. Morphological findings in the liver of children with cystic fibrosis: A light and electron microscopical study
  255. Absence of prostaglandins in semen of men with cystic fibrosis is an indication of the contribution of the seminal vesicles
  256. Conformity of bacterial growth in sputum and contamination free endobronchial samples in patients with cystic fibrosis.
  257. LIVER DAMAGE IN JUVENILE INFLAMMATORY BOWEL DISEASE
  258. Physical activity and self treatment in cystic fibrosis.
  259. Increased mole fraction of arachidonic acid in bronchial phospholipids in patients with cystic fibrosis
  260. Antibodies to Staphylococcal Teichoic Acid and Alpha Toxin in Patients with Cystic Fibrosis
  261. In vivo and vitro studies on formation of bile acids in patients with Zellweger syndrome. Evidence that peroxisomes are of importance in the normal biosynthesis of both cholic and chenodeoxycholic acid.
  262. Relation between antibody response to pseudomonas aeruginosa exoproteins and colonization/infection in patients with cystic fibrosis
  263. Nutritional status in children receiving home parenteral nutrition
  264. Unsuccessful Attempts to Induce Peroxisomes in Two Cases of Zellweger Disease by Treatment with Clofibrate
  265. 638 NUTRITION STATUS INF ED AND UNDFED CHILDREN RECEIVING HOME PARENTERAL
  266. Fasting Serum Bile Acid Levels in Relation to Liver Histopathology in Cystic Fibrosis
  267. Relation between Antibody Response to Pseudomonas aeruginosa Exoproteins and Colonization/Infection in Patients with Cystic Fibrosis
  268. Urinary excretion of dicarboxylic acids from patients with the zellweger syndrome Importance of peroxisomes in β-oxidation of dicarboxylic acids
  269. Persistent Tyrosinemia Associated with Low Activity of Tyrosine Aminotransferase
  270. ADVERSE REACTIONS TO PIPERACILLIN IN PATIENTS WITH CYSTIC FIBROSIS
  271. Urinary excretion of tetrahydroxylated bile acids in children with α1-antitrypsin deficiency and neonatal cholestasis
  272. Prospective Study of Fatty Acid Supplementation Over 3 Years in Patients with Cystic Fibrosis
  273. DIFFERENCE IN RENAL HANDLING OF CEFSULODIN BETWEEN PATIENTS WITH CYSTIC FIBROSIS AND NORMAL SUBJECTS
  274. Clinical results and pharmacokinetics of ceftazidime treatment in patients with cystic fibrosis
  275. Alpha-1-antitrypsin deficiency and juvenile liver disease Ultrastructural observations compared with light microscopy and routine liver tests
  276. Serum Bile Acids as Markers of Juvenile Liver Disease in α1-Antitrypsin Deficiency
  277. LIVER DISEASE IN CHILDREN WITH ALPHA1-ANTITRYPSIN DEFICIENCY WITHOUT NEONATAL CHOLESTASIS
  278. NATURAL HISTORY OF CHILDREN WITH ALPHA1‐ANTITRYPSIN DEFICIENCY AND NEONATAL CHOLESTASIS
  279. Urinary excretion of bile alcohols in normal children and patients with α1‐antitrypsin deficiency during development of liver disease
  280. RENAL FUNCTION IN CYSTIC FIBROSIS WITH SPECIAL REFERENCE TO THE RENAL SODIUM HANDLING
  281. Tetrahydroxylated bile acids in healthy human newborns
  282. BILE ACID METABOLISM IN LOW BIRTHWEIGHT INFANTS
  283. RENAL DISTURBANCE IN CYSTIC FIBROSIS
  284. THE FIRST INFANT TO SURVIVE A GENERALIZED BCG INFECTION
  285. RENAL FUNCTION IN CYSTIC FIBROSIS
  286. Excretion of bile acids in healthy children and children with cystic fibrosis
  287. Urinary Bile Acid Excretion in Correlation to Liver Histopathology in Cystic Fibrosis
  288. METABOLISM OF LITHOCHOLIC ACID‐24–14C IN EXTRAHEPATIC BILIARY ATRESIA
  289. URINARY BILE ACID CONJUGATES IN EXTRAHEPATIC BILIARY ATRESIA
  290. BILE ACID EXCRETION AFTER DISAPPEARANCE OF JAUNDICE IN INTRAHEPATIC CHOLESTASIS OF INFANCY
  291. EXCRETION OF BILE ACIDS IN EXTRAHEPATIC BILIARY ATRESIA AND INTRAHEPATIC CHOLESTASIS OF INFANCY
  292. EXCRETION OF BILE ACIDS IN ERYTHROBLASTOSIS FOETALIS
  293. BILE ACIDS AND PANCREATIC ENZYMES DURING ABSORPTION IN THE NEWBORN
  294. Excretion of 3β-hydroxy-5-cholenoic and 3a-hydroxy-5a-cholanoic acids in urine of infants with biliary atresia
  295. TEST‐MEAL IN THE DIAGNOSIS OF MALABSORPTION IN INFANCY
  296. INTRAVENOUS GLUCOSE TOLERANCE IN OVERWEIGHT NEWBORN INFANTS AND THEIR MOTHERS
  297. BILE ACID EXCRETION AND MALABSORPTION IN INTRAHEPATIC CHOLESTASIS OF INFANCY (“NEONATAL HEPATITIS”)
  298. AMAUROSIS AFTER BROXYQUINOLINE
  299. Hepatobiliary Disease in Cystic Fibrosis