A rare syndrome of bone fibrous dysplasia associated with intramuscular myxomas.

What is it about?

This form of fibrous dysplasia, generally localized to pelvis and femur, results in a fragile bone with deformities, pain, pathological fractures and functional impairment. Intramuscular myxomas, generally rare benign mesenchymal neoplasms, exceptionally may evolve to malignant forms.

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Why is it important?

Zoledronic acid therapy rapidly lowered bone pain together with a reduction of intramuscular myxoma volume.

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