What is it about?
A case report of 2 patients with isolated left subclavian artery from the pulmonary artery who presented with stridor. The first patient also had tetralogy of Fallot, pulmonary artery sling,bilateral superior caval veins and left bronchial isomerism suggesting heterotaxy syndrome. While the second patient had a right aortic arch, isolated left subclavian artery and bilateral arterial ducts. It discussed if isolated left subclavian artery really causes vascular ring?
Featured Image
Why is it important?
The first reported cases of isolated left subclavian artery associated with upper airway obstruction symptoms. It also the first reported case of single stage operation consisted of tetralogy of Fallot repair, reimplantation of the left pulmonary artery to main pulmonary artery and reimplantation of left subclavian artery to left common carotid artery.
Perspectives
This case reports highlighting the importance of a high index of clinical suspicion in our routine management of a patient.Whenever symptoms are not readily explained by the obvious congenital heart defects, a careful examination of the pulmonary anatomy, the aortic arch and its branching pattern should be assessed to rule out a lesion that may be causing or associated with airway compressions to avoid unnecessary delay in diagnosis
Dr Putri Yubbu
University Putra Malaysia
Read the Original
This page is a summary of: Right aortic arch with isolation of the left subclavian artery: a rare association with airway obstruction, Cardiology in the Young, November 2016, Cambridge University Press,
DOI: 10.1017/s1047951116001840.
You can read the full text:
Contributors
The following have contributed to this page
