All Stories

  1. Impact of Discontinuing Both Hypertonic Saline and Dornase Alfa after Elexacaftor-Tezacaftor-Ivacaftor in Cystic Fibrosis
  2. Predicting weight gain in patients with cystic fibrosis on triple combination modulator
  3. A comparison of aminoglycoside antibiotic serum concentrations collected by peripheral veins and peripherally inserted central catheters in adults with cystic fibrosis
  4. Airway inflammation accelerates pulmonary exacerbations in cystic fibrosis
  5. Mutations in the C-terminal region of the bacteriophage exclusion protein PglX can selectively inactivate restriction in Salmonella
  6. Inhaled mRNA therapy for treatment of cystic fibrosis: Interim results of a randomized, double‐blind, placebo‐controlled phase 1/2 clinical study
  7. Lung Function Decline in Cystic Fibrosis: Impact of Data Availability and Modeling Strategies on Clinical Interpretations
  8. Safety and efficacy of vanzacaftor–tezacaftor–deutivacaftor in adults with cystic fibrosis: randomised, double-blind, controlled, phase 2 trials
  9. Calibration and validation of modeled 5-year survival predictions among people with cystic fibrosis treated with the cystic fibrosis transmembrane conductance regulator modulator ivacaftor using United States registry data
  10. Discontinuation versus continuation of hypertonic saline or dornase alfa in modulator treated people with cystic fibrosis (SIMPLIFY): results from two parallel, multicentre, open-label, randomised, controlled, non-inferiority trials
  11. Associations of Sputum Biomarkers with Clinical Outcomes in People with Cystic Fibrosis
  12. Spotlighting “Neutrophil Elastase Triggers the Release of Macrophage Extracellular Traps”: A New Catch in Cystic Fibrosis?
  13. Forced Expiratory Flow at 25%-75% Links COPD Physiology to Emphysema and Disease Severity in the SPIROMICS Cohort
  14. Enhanced epithelial sodium channel activity in neonatal Scnn1b mouse lung attenuates high oxygen-induced lung injury
  15. Long-term safety and efficacy of tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study
  16. Hypoxia induces expression of angiotensin‐converting enzyme II in alveolar epithelial cells: Implications for the pathogenesis of acute lung injury in COVID‐19
  17. SARS‐CoV‐2 innate effector associations and viral load in early nasopharyngeal infection
  18. The Uncertain Role of Corticosteroids in the Treatment of COVID-19
  19. SARS-CoV-2 Innate Effector Associations and Viral Load in Early Nasopharyngeal Infection
  20. Impact of low-level fine particulate matter and ozone exposure on absences in K-12 students and economic consequences
  21. Evaluation of a five-year predicted survival model for cystic fibrosis in later time periods
  22. High-mobility group box-1 increases epithelial sodium channel activity and inflammation via the receptor for advanced glycation end products
  23. Refinement of metabolite detection in cystic fibrosis sputum reveals heme correlates with lung function decline
  24. A multi-scale approach to study biochemical and biophysical aspects of resveratrol on diesel exhaust particle-human primary lung cell interaction
  25. Longer Life or More Life: Choose One Please
  26. Prospective multicenter randomized patient recruitment and sample collection to enable future measurements of sputum biomarkers of inflammation in an observational study of cystic fibrosis
  27. RV/LV ratio in severe sepsis and septic shock: Response to Letter to the Editor
  28. The Clinical Biology of Cystic Fibrosis Transmembrane Regulator Protein
  29. Modeling long-term health outcomes of patients with cystic fibrosis homozygous for F508del-CFTR treated with lumacaftor/ivacaftor
  30. Right-to-left ventricular end diastolic diameter ratio in severe sepsis and septic shock
  31. Refinement of metabolite detection in cystic fibrosis sputum reveals heme negatively correlates with lung function
  32. Pharmacokinetics of Continuous Infusion Beta-lactams in the Treatment of Acute Pulmonary Exacerbations in Adult Patients With Cystic Fibrosis
  33. Population Pharmacokinetics of Amikacin in Adult Patients with Cystic Fibrosis
  34. Thailandamide, a Fatty Acid Synthesis Antibiotic That Is Coexpressed with a Resistant Target Gene
  35. Micro-organisms that live in the airway of CF patients interact with each other
  36. Cystic Fibrosis Colorectal Cancer Screening Consensus Recommendations
  37. Sleep Phase Delay in Cystic Fibrosis
  38. The Dynamics of Disease Progression in Cystic Fibrosis
  39. Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium
  40. Forced Expiratory Volume in 1 Second Variability Helps Identify Patients with Cystic Fibrosis at Risk of Greater Loss of Lung Function
  41. Adolescents with cystic fibrosis: Take the door, not the window
  42. Rib plating of acute and sub-acute non-union rib fractures in an adult with cystic fibrosis: a case report
  43. Genetic Discovery, Rigorous Statistics, and Pandemic Influenza
  44. Use of older donors for lung transplantation—you can’t get there from here
  45. Lung transplantation for chronic obstructive pulmonary disease
  46. Toxicity effects of short term diesel exhaust particles exposure to human small airway epithelial cells (SAECs) and human lung carcinoma epithelial cells (A549)
  47. Ivacaftor in Subjects With Cystic Fibrosis Who Are Homozygous for the F508del-CFTR Mutation
  48. Sputum Biomarkers and the Prediction of Clinical Outcomes in Patients with Cystic Fibrosis
  49. Delay in Recognition of Pulmonary Arterial Hypertension
  50. Denufosol Tetrasodium in Patients with Cystic Fibrosis and Normal to Mildly Impaired Lung Function
  51. The Changing Picture of Patients With Pulmonary Arterial Hypertension in the United States
  52. Predicting Survival in Pulmonary Arterial Hypertension
  53. Year-to-year changes in lung function in individuals with cystic fibrosis
  54. Pulmonary Arterial Hypertension
  55. Efficacy and Safety of a New Formulation of Pancrelipase (Ultrase MT20) in the Treatment of Malabsorption in Exocrine Pancreatic Insufficiency in Cystic Fibrosis
  56. Carrier Screening, Incidence of Cystic Fibrosis, and Difficult Decisions
  57. Lung Transplantation for Cystic Fibrosis
  58. Insulin Therapy to Improve BMI in Cystic Fibrosis-Related Diabetes Without Fasting Hyperglycemia: Results of the Cystic Fibrosis Related Diabetes Therapy Trial
  59. Spirometry
  60. Measurement of Lung Volumes
  61. Pediatric Lung Transplantation for Cystic Fibrosis
  62. Design of the REVEAL Registry for US Patients With Pulmonary Arterial Hypertension
  63. Outcomes of Care by Hospitalists
  64. Lung Transplantation and Survival in Children with Cystic Fibrosis
  65. A phase 2 study of aztreonam lysine for inhalation to treat patients with cystic fibrosis andPseudomonas aeruginosa infection
  66. Lung transplantation for cystic fibrosis
  67. BIVENTRICULAR FAILURE POST TAMPONADE DRAINAGE IN A PATIENT WITH SYSTEMIC LUPUS ERYTHEMATOSUS AND PULMONARY HYPERTENSION
  68. Epidemiology of cystic fibrosis-related diabetes
  69. Use of Lung Transplantation Survival Models to Refine Patient Selection in Cystic Fibrosis
  70. Selection of patients with cystic fibrosis for lung transplantation
  71. Predictive 5-Year Survivorship Model of Cystic Fibrosis
  72. Nonisotropic Enzyme-Inhibitor Interactions: A Novel Nonoxidative Mechanism for Quantum Proteolysis by Human Neutrophils