All Stories

  1. A grumbling concern: A survey of gastrointestinal symptoms in cystic fibrosis in the modulator era

    Article • NIHR Open Research, February 2024, National Institute for Health Research

    Siobhan Carr

  2. Impact of elexacaftor/tezacaftor/ivacaftor on fat-soluble vitamin levels in children with cystic fibrosis

    Article • Journal of Cystic Fibrosis, September 2023, Elsevier

    Siobhan Carr

  3. Factors associated with within-individual variability of lung function for people with cystic fibrosis: a longitudinal registry study

    Article • May 2023, Cold Spring Harbor Laboratory Press

    Siobhan Carr

  4. Trajectories of early growth and subsequent lung function in cystic fibrosis: An observational study using UK and Canadian registry data

    Article • Journal of Cystic Fibrosis, May 2023, Elsevier

    Siobhan Carr

  5. A grumbling concern: an international survey of gastrointestinal symptoms in cystic fibrosis in the modulator era

    Article • NIHR Open Research, April 2023, National Institute for Health Research

    Siobhan Carr

  6. Response

    Article • CHEST Journal, April 2023, Elsevier

    Siobhan Carr

  7. Future therapies for cystic fibrosis

    Article • Nature Communications, February 2023, Springer Science + Business Media

    Siobhan Carr

  8. The Impact on Parents of Diagnosing PCD in Young Children

    Article • Journal of Clinical Medicine, August 2022, MDPI AG

    Siobhan Carr

  9. Factors associated with clinical progression to severe COVID-19 in people with cystic fibrosis: A global observational study

    Article • Journal of Cystic Fibrosis, July 2022, Elsevier

    Siobhan Carr

  10. The disease-specific clinical trial network for primary ciliary dyskinesia: PCD-CTN

    Article • ERJ Open Research, June 2022, European Respiratory Society (ERS)

    Siobhan Carr

  11. Initiating home spirometry for children during the COVID-19 pandemic – A practical guide

    Article • Paediatric Respiratory Reviews, June 2022, Elsevier

    Siobhan Carr

  12. Exploring the nature of perceived treatment burden: a study to compare treatment burden measures in adults with cystic fibrosis

    Article • NIHR Open Research, May 2022, National Institute for Health Research

    Siobhan Carr

  13. Childhood bronchiectasis, so little is known

    Article • Archives of Disease in Childhood, March 2022, BMJ

    Siobhan Carr

  14. Incidence and risk factors of cancer in individuals with cystic fibrosis in the UK; a case-control study

    Article • Journal of Cystic Fibrosis, March 2022, Elsevier

    Siobhan Carr

  15. Using Negative Control Outcomes and Difference-in-Differences Analysis to Estimate Treatment Effects in an Entirely Treated Cohort: The Effect of Ivacaftor in Cystic Fibrosis

    Article • American Journal of Epidemiology, November 2021, Oxford University Press (OUP)

    Siobhan Carr

  16. Factors for severe outcomes following SARS-CoV-2 infection in people with cystic fibrosis in Europe

    Article • ERJ Open Research, October 2021, European Respiratory Society (ERS)

    Siobhan Carr

  17. COVID-19 vaccine prioritisation for people with cystic fibrosis

    Article • Journal of Cystic Fibrosis, July 2021, Elsevier

    Siobhan Carr

  18. Clinical characteristics of Pseudomonas and Aspergillus co-infected cystic fibrosis patients: A UK registry study

    Article • Journal of Cystic Fibrosis, May 2021, Elsevier

    Dr Dominic Hughes, Siobhan Carr

  19. Survival estimates in European cystic fibrosis patients and the impact of socioeconomic factors: a retrospective registry cohort study

    Article • European Respiratory Journal, March 2021, European Respiratory Society (ERS)

    Siobhan Carr

  20. Eradication success for non-tuberculous mycobacteria in children with cystic fibrosis

    Article • European Respiratory Journal, February 2021, European Respiratory Society (ERS)

    Dr Dominic Hughes, Siobhan Carr

  21. Learning to breathe with Tai Chi online - qualitative data from a randomized controlled feasibility study of patients with cystic fibrosis

    Article • European Journal of Integrative Medicine, October 2020, Elsevier

    Prof Nicola Robinson, Siobhan Carr

  22. An observational study of the lung clearance index throughout childhood in cystic fibrosis: early years matter

    Article • European Respiratory Journal, May 2020, European Respiratory Society (ERS)

    Gwyneth Davies, Siobhan Carr

  23. Combination antifungal therapy for Scedosporium species in cystic fibrosis

    Article • Pediatric Pulmonology, April 2020, Wiley

    Siobhan Carr

  24. Registries and collaborative studies for primary ciliary dyskinesia in Europe

    Article • ERJ Open Research, April 2020, European Respiratory Society (ERS)

    Claudia Kuehni, Cristina Ardura-Garcia, Siobhan Carr

  25. Fair selection of participants in clinical trials: The challenge to push the envelope further

    Article • Journal of Cystic Fibrosis, September 2019, Elsevier

    Siobhan Carr

  26. Non-invasive ventilation and clinical outcomes in cystic fibrosis: Findings from the UK CF registry

    Article • Journal of Cystic Fibrosis, September 2019, Elsevier

    Siobhan Carr

  27. Time trends in diagnostic testing for primary ciliary dyskinesia in Europe

    Article • European Respiratory Journal, July 2019, European Respiratory Society (ERS)

    Claudia Kuehni, Henryk Mazurek, Siobhan Carr

  28. The prevalence, clinical status and genotype of cystic fibrosis patients living in Cuba using national registry data

    Article • Journal of Cystic Fibrosis, July 2019, Elsevier

    Siobhan Carr

  29. Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations

    Article • Journal of Cystic Fibrosis, May 2019, Elsevier

    Siobhan Carr

  30. Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

    Article • ERJ Open Research, February 2019, European Respiratory Society (ERS)

    Siobhan Carr

  31. Identifying exceptional cystic fibrosis care services: combining statistical process control with focus groups

    Article • Health Services and Delivery Research, February 2019, National Institute for Health Research

    Siobhan Carr

  32. The Proceedings of the 16th Italian Convention of Investigators in Cystic Fibrosis

    Article • Multidisciplinary Respiratory Medicine, February 2019, Mattioli1885

    Siobhan Carr

  33. Investigating the effects of long-term dornase alfa use on lung function using registry data

    Article • Journal of Cystic Fibrosis, January 2019, Elsevier

    Siobhan Carr

  34. Quantifying fluctuation in glucose levels to identify early changes in glucose homeostasis in cystic fibrosis

    Article • Journal of Cystic Fibrosis, November 2018, Elsevier

    Siobhan Carr

  35. Children and Adults Tai Chi Study (CF-CATS2): a randomised controlled feasibility study comparing internet-delivered with face-to-face Tai Chi lessons in cystic fibrosis

    Article • ERJ Open Research, October 2018, European Respiratory Society (ERS)

    Siobhan Carr, Prof Nicola Robinson

  36. Impact of cystic fibrosis on birthweight: a population based study of children in Denmark and Wales

    Article • Thorax, July 2018, BMJ

    Siobhan Carr

  37. Use of a rare disease patient registry in long-term post-authorisation drug studies: a model for collaboration with industry

    Article • The Lancet Respiratory Medicine, July 2018, Elsevier

    Siobhan Carr

  38. Hypersensitivity reactions to intravenous antibiotics in cystic fibrosis

    Article • Paediatric Respiratory Reviews, June 2018, Elsevier

    Siobhan Carr

  39. Primary Ciliary Dyskinesia Due to Microtubular Defects is Associated with Worse Lung Clearance Index

    Article • Lung, January 2018, Springer Science + Business Media

    Siobhan Carr

  40. Pulmonary function deficits in newborn screened infants with cystic fibrosis managed with standard UK care are mild and transient

    Article • European Respiratory Journal, November 2017, European Respiratory Society (ERS)

    Gwyneth Davies, Siobhan Carr

  41. Data Resource Profile: The UK Cystic Fibrosis Registry

    Article • International Journal of Epidemiology, October 2017, Oxford University Press (OUP)

    Siobhan Carr

  42. Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia

    Article • Pediatric Pulmonology, June 2016, Wiley

    Siobhan Carr

  43. Paranasal sinus pathogens in children with cystic fibrosis: Do they relate to lower respiratory tract pathogens and is eradication successful?

    Article • Journal of Cystic Fibrosis, July 2014, Elsevier

    Siobhan Carr

  44. The impact of switching to the new global lung function initiative equations on spirometry results in the UK CF Registry

    Article • Journal of Cystic Fibrosis, May 2014, Elsevier

    Siobhan Carr

  45. Diagnosis and management of primary ciliary dyskinesia

    Article • Archives of Disease in Childhood, April 2014, BMJ

    Siobhan Carr

  46. Diagnosis of cystic fibrosis in London and South East England before and after the introduction of newborn screening

    Article • Archives of Disease in Childhood, November 2013, BMJ

    Siobhan Carr

  47. Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening

    Article • Thorax, June 2012, BMJ

    Siobhan Carr

  48. Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF

    Article • Thorax, March 2011, BMJ

    Siobhan Carr

  49. Lung Clearance Index at 4 Years Predicts Subsequent Lung Function in Children with Cystic Fibrosis

    Article • American Journal of Respiratory and Critical Care Medicine, March 2011, American Thoracic Society

    Siobhan Carr

  50. Non-cystic fibrosis bronchiectasis: its diagnosis and management

    Article • Archives of Disease in Childhood Education & Practice, May 2010, BMJ

    Siobhan Carr

  51. Growth in children with cystic fibrosis‐related diabetes

    Article • Pediatric Pulmonology, November 2009, Wiley

    Siobhan Carr

  52. Lung Function from Infancy to the Preschool Years after Clinical Diagnosis of Cystic Fibrosis

    Article • American Review of Respiratory Disease, July 2008, American Thoracic Society

    Professor Sarath C Ranganathan, Siobhan Carr

  53. Early detection of cystic fibrosis lung disease: multiple-breath washout versus raised volume tests

    Article • Thorax, January 2007, BMJ

    Siobhan Carr

  54. A comparison of the prevalence of urinary incontinence in girls with cystic fibrosis, asthma, and healthy controls

    Article • Pediatric Pulmonology, September 2006, Wiley

    Siobhan Carr

  55. Growth and lung function in Asian patients with cystic fibrosis

    Article • Archives of Disease in Childhood, June 2005, BMJ

    Siobhan Carr

  56. Relative Ability of Full and Partial Forced Expiratory Maneuvers to Identify Diminished Airway Function in Infants with Cystic Fibrosis

    Article • American Review of Respiratory Disease, November 2002, American Thoracic Society

    Professor Sarath C Ranganathan, Siobhan Carr

  57. Airway function in infants newly diagnosed with cystic fibrosis

    Article • The Lancet, December 2001, Elsevier

    Siobhan Carr

  58. Reproductive health in males with cystic fibrosis: Knowledge, attitudes, and experience of patients and parents

    Article • Pediatric Pulmonology, April 1999, Wiley

    Siobhan Carr

  59. An evaluation of two aerosol delivery systems for rhDNase

    Article • European Respiratory Journal, June 1997, European Respiratory Society (ERS)

    Siobhan Carr