All Stories

  1. Genetic Screening of Patients With Inherited Fanconi Syndrome
  2. Retinoic Acid-inducible Gene-I Increases Interferon-stimulated Gene 15 Expression in Human Renal Proximal Tubule Epithelial Cells
  3. Recurrent C3 glomerulopathy after prolonged remission
  4. Toll‐Like Receptor 3 Activation in Lupus Nephritis: A Renal Signature Supporting “Pseudoviral” Immunity
  5. Unveiling long-standing low-molecular-weight proteinuria: A proximal tubular mitochondrial enzyme impairment caused by EHHADH mutation
  6. Tripartite motif 22 (TRIM22) downregulates TLR3-induced CCL5 expression in human renal proximal tubular epithelial cells
  7. Long‐term outcome of tacrolimus‐based immunosuppressive treatment for patients with paediatric‐onset lupus nephritis
  8. Recovery from rituximab-associated persistent hypogammaglobulinaemia in children with nephrotic syndrome
  9. Cylindromatosis lysine 63 deubiquitinase (CYLD) suppress TLR3-mediated CCL5 expression in human renal proximal tubular epithelial cells
  10. Interferon‐stimulated gene 56 positively regulates Toll‐like receptor 3‐mediated CXCL10 expression in human renal proximal tubular epithelial cells
  11. Early add-on use of belimumab as induction therapy for patients with childhood-onset systemic lupus erythematosus
  12. Clinical Characteristics of Cryopyrin‐Associated Periodic Syndrome and Long‐Term Real‐World Efficacy and Tolerability of Canakinumab in Japan: Results of a Nationwide Survey
  13. Be aware of severe juvenile chronic iridocyclitis without evidence of arthritis: Juvenile chronic iridocyclitis revisited
  14. Expression of interferon-stimulated gene 20 (ISG20), an antiviral effector protein, in glomerular endothelial cells: possible involvement of ISG20 in lupus nephritis
  15. Long-term outcome of tacrolimus monotherapy in a patient with lupus nephritis: A 12-year observation
  16. Glomerular endothelial expression of type I IFN-stimulated gene, DExD/H-Box helicase 60 via toll-like receptor 3 signaling: possible involvement in the pathogenesis of lupus nephritis
  17. Underrecognized Frasier syndrome revisited: Paradoxical immunocomplex deposition
  18. Be aware of underlying Dent disease in young boys with massive proteinuria
  19. Interleukin-6 via Toll-Like Receptor 3 Signaling Attenuates the Expression of Proinflammatory Chemokines in Human Podocytes
  20. Inhibitory effect of anti-malarial agents on the expression of proinflammatory chemokines via Toll-like receptor 3 signaling in human glomerular endothelial cells
  21. Podocyte sphingomyelin phosphodiesterase acid-like 3b decreases among children with idiopathic nephrotic syndrome
  22. Orthostatic proteinuria revisited: new clinical impact of the “old” clinical entity?
  23. Interferon-induced transmembrane protein 1 and Myxovirus resistance protein 1 are induced by polyinosinic-polycytidylic acid in cultured hCMEC/D3 human cerebral microvascular endothelial cells
  24. Endothelial expression of fractalkine (CX3CL1) is induced by Toll-like receptor 3 signaling in cultured human glomerular endothelial cells
  25. Complete clinical resolution of a Japanese family with renal pseudohypoaldosteronism type 1 due to a novel NR3C2 mutation
  26. High prevalence of underlying orthostatic proteinuria in young Japanese women
  27. Induction of C‐C motif chemokine ligand 2 through Toll‐like receptor 3 signaling in human cerebral microvascular endothelial cell/D3 cells: possible regulation by nuclear factor‐κB
  28. Fatal case of Hajdu-Cheney syndrome with idiopathic pulmonary hemosiderosis
  29. Cytosolic Sensors of Viral RNA Are Involved in the Production of Interleukin-6 via Toll-Like Receptor 3 Signaling in Human Glomerular Endothelial Cells
  30. Overweight Children at a Primary School in Hirosaki City: A Longitudinal, Individualized, Observational Study
  31. Interferon-stimulated gene 60 (ISG60) constitutes a negative feedback loop in the downstream of TLR3 signaling in hCMEC/D3 cells
  32. Chloroquine attenuates TLR3-mediated plasminogen activator inhibitor-1 expression in cultured human glomerular endothelial cells
  33. <b>Gnetin C suppresses double-stranded RNA-induced C-C motif chemokine ligand 2 (CCL2) and CCL5 production by inhibiting Toll-like receptor 3 signaling </b><b>pathway </b>
  34. Long-term clinicopathologic observation in a case of steroid-resistant nephrotic syndrome caused by a novel Crumbs homolog 2 mutation
  35. <b>Gnetin C, a resveratrol dimer, reduces amyloid-β 1–42 (Aβ42) production and ameliorates Aβ42-lowered cell viability in cultured SH-SY5Y human neuroblastoma </b><b>cells </b>
  36. Retinoic acid-inducible gene-I, melanoma differentiation-associated gene 5 and C-X-C motif chemokine ligand 10 are induced by a Toll-like receptor 3 agonist in human brain microvascular endothelial cells
  37. Toll-Like Receptor 3 Signaling Contributes to Regional Neutrophil Recruitment in Cultured Human Glomerular Endothelial Cells
  38. Free light chain-associated Fanconi syndrome in an adolescent
  39. Rebamipide reduces amyloid-β 1–42 (Aβ42) production and ameliorates Aβ43-lowered cell viability in cultured SH-SY5Y human neuroblastoma cells
  40. Urinary excretion of sphingomyelinase phosphodiesterase acid-like 3b in children with intractable nephrotic syndrome
  41. Expression of CCL5 is induced by polyinosinic : polycytidylic acid in cultured hCMEC/D3 human brain microvascular endothelial cells
  42. Treatment of pediatric-onset lupus nephritis: a proposal of optimal therapy
  43. Interferon (IFN)-induced protein 35 (IFI35) negatively regulates IFN-β-phosphorylated STAT1-RIG-I-CXCL10/CCL5 axis in U373MG astrocytoma cells treated with polyinosinic-polycytidylic acid
  44. Post-acute ischemic change and colon stricture in hemolytic uremic syndrome
  45. Chloroquine attenuates TLR3/IFN-β signaling in cultured normal human mesangial cells: A possible protective effect against renal damage in lupus nephritis
  46. Cylindromatosis (CYLD), a Deubiquitinase, Attenuates Inflammatory Signaling Pathways by Activating Toll-Like Receptor 3 in Human Mesangial Cells
  47. <b>DEC1 negatively regulates the expression of CXCL10 and CCL5 induced by poly IC in normal human mesangial </b><b>cells </b>
  48. Clarithromycin attenuates the expression of monocyte chemoattractant protein-1 by activating toll-like receptor 4 in human mesangial cells
  49. Hyper-IgE syndrome with a novel mutation of the STAT3 gene
  50. Does Dent disease remain an underrecognized cause for young boys with focal glomerulosclerosis?
  51. Monitoring of Epstein–Barr virus load and killer T cells in patients with juvenile idiopathic arthritis treated with methotrexate or tocilizumab
  52. Interferon-stimulated gene (ISG) 60, as well as ISG56 and ISG54, positively regulates TLR3/IFN-β/STAT1 axis in U373MG human astrocytoma cells
  53. Interferon (IFN)-Induced Protein 35 (IFI35), a Type I Interferon-Dependent Transcript, Upregulates Inflammatory Signaling Pathways by Activating Toll-Like Receptor 3 in Human Mesangial Cells
  54. Interferon-Stimulated Gene 15, a Type I Interferon-Dependent Transcript, Is Involved in a Negative Feedback Loop in Innate Immune Reactions in Human Mesangial Cells
  55. Expressions of mRNA for innate immunity-associated functional molecules in urinary sediment in immunoglobulin A nephropathy
  56. Carnosic acid attenuates apoptosis induced by amyloid-β 1–42 or 1–43 in SH-SY5Y human neuroblastoma cells
  57. Desferrioxamine, an iron chelator, inhibits CXCL10 expression induced by polyinosinic–polycytidylic acid in U373MG human astrocytoma cells
  58. Alteration in the podoplanin–ezrin–cytoskeleton linkage is an important initiation event of the podocyte injury in puromycin aminonucleoside nephropathy, a mimic of minimal change nephrotic syndrome
  59. Severe intrinsic acute kidney injury associated with therapeutic doses of acetaminophen
  60. Mizoribine in the treatment of pediatric-onset glomerular disease
  61. Toll-like receptor 3 signaling contributes to the expression of a neutrophil chemoattractant, CXCL1 in human mesangial cells
  62. ISG54 and ISG56 are induced by TLR3 signaling in U373MG human astrocytoma cells: Possible involvement in CXCL10 expression
  63. Efficacy of mizoribine-tacrolimus-based induction therapy for pediatric lupus nephritis
  64. Tumor necrosis factor-α synergistically enhances polyinosinic-polycytidylic acid-induced toll-like receptor 3 signaling in cultured normal human mesangial cells: possible involvement in the pathogenesis of lupus nephritis
  65. Carnosic acid suppresses the production of amyloid-β 1-42 and 1-43 by inducing an α-secretase TACE/ADAM17 in U373MG human astrocytoma cells
  66. Efficacy of long-term multidrug therapy in a patient with focal segmental glomerulosclerosis
  67. Mizoribine selectively attenuates monocyte chemoattractant protein-1 production in cultured human glomerular mesangial cell: A possible benefit of its use in the treatment of lupus nephritis
  68. Glomerular expression of myxovirus resistance protein 1 in human mesangial cells: Possible activation of innate immunity in the pathogenesis of lupus nephritis
  69. Single dose of rituximab for pediatric-onset refractory systemic lupus erythematosus
  70. Severe post-streptococcal acute glomerulonephritis and periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome
  71. Long-Term Tacrolimus-Based Immunosuppressive Treatment for Young Patients with Lupus Nephritis: A Prospective Study in Daily Clinical Practice
  72. Inflammatory Chemokine Expression via Toll-Like Receptor 3 Signaling in Normal Human Mesangial Cells
  73. Interaction between Interferon-Stimulated Gene 56 and Melanoma Differentiation-Associated Gene 5 in Toll-Like Receptor 3 Signaling in Normal Human Mesangial Cells
  74. TLR4 signaling induces retinoic acid-inducible gene-I and melanoma differentiation-associated gene 5 in mesangial cells
  75. Urinary Fractalkine and Monocyte Chemoattractant Protein-1 as Possible Predictors of Disease Activity of Childhood Glomerulonephritis
  76. A young girl with refractory intestinal Behçet’s disease: a case report and review of literatures on pediatric cases who received an anti-tumor necrosis factor agent
  77. Persistent Immature Glomeruli in a Girl with Refractory Nephrotic Syndrome
  78. Glomerular expression of fractalkine is induced by polyinosinic-polycytidylic acid in human mesangial cells: possible involvement of fractalkine after viral infection
  79. Long-term multidrug therapy in an adolescent patient with proliferative lupus nephritis: a trial of less cytotoxic therapy
  80. Treatment of young patients with lupus nephritis using calcineurin inhibitors
  81. Melanoma Differentiation-Associated Gene 5 Regulates the Expression of a Chemokine CXCL10 in Human Mesangial Cells: Implications for Chronic Inflammatory Renal Diseases
  82. Imbalance towards Th1 pathway predominance in purpura nephritis with proteinuria
  83. Autoantibodies to villin occur frequently in IPEX, a severe immune dysregulation, syndrome caused by mutation of FOXP3
  84. Polyinosinic-Polycytidylic Acid Induces the Expression of Interferon-Stimulated Gene 20 in Mesangial Cells
  85. Novel multidrug therapy for children with cyclosporine-resistant or -intolerant nephrotic syndrome
  86. Tacrolimus monotherapy in a patient with lupus flare using once-daily administration protocol
  87. Basic-helix-loop-helix transcription factor DEC2 constitutes negative feedback loop in IFN-β-mediated inflammatory responses in human mesangial cells
  88. Addition of mizoribine to the prednisolone plus tacrolimus treatment regimen in a patient with lupus flare
  89. Successful Multidrug Treatment of a Pediatric Patient with Severe Churg-Strauss Syndrome Refractory to Prednisolone
  90. Clinical responses to EGFR-tyrosine kinase inhibitor retreatment in non-small cell lung cancer patients who benefited from prior effective gefitinib therapy: a retrospective analysis
  91. Efficacy and safety of tacrolimus in 101 consecutive patients with rheumatoid arthritis: a possible alternative treatment to methotrexate?
  92. Retinoic acid-inducible gene-I is induced by double-stranded RNA and regulates the expression of CC chemokine ligand (CCL) 5 in human mesangial cells
  93. Mizoribine attenuates renal injury and macrophage infiltration in patients with severe lupus nephritis
  94. Potential Th1/Th2 predominance in children with newly diagnosed IgA nephropathy
  95. Intravenous immunoglobulin therapy leading to dramatic improvement in a patient with systemic juvenile idiopathic arthritis and severe pericarditis resistant to steroid pulse therapy
  96. Retinoic acid-inducible gene-I (RIG-I) is induced by IFN-  in human mesangial cells in culture: possible involvement of RIG-I in the inflammation in lupus nephritis
  97. Benefits of Once-Daily Administration of Cyclosporine A for Children with Steroid-Dependent, Relapsing Nephrotic Syndrome
  98. IFN-γ and TNF-α Synergistically Induce microRNA-155 Which Regulates TAB2/IP-10 Expression in Human Mesangial Cells
  99. Use of recombinant human serum albumin in pediatric patients with nephrotic syndrome
  100. A novel multidrug therapy for difficult cyclosporine-resistant focal segmental glomerulosclerosis
  101. Mizoribine Treatment of Young Patients with Severe Lupus Nephritis: A Clinicopathologic Study by the Tohoku Pediatric Study Group
  102. Vesical varices and telangiectasias in a patient with ataxia telangiectasia
  103. Effective treatment of young patients with pediatric-onset, long-standing lupus nephritis with tacrolimus given as a single daily dose: an open-label pilot study
  104. Long-term intermittent pulse therapy with mizoribine attenuates histologic progression in young patients with severe lupus nephritis: Report of two patients (Brief Communication)
  105. Mizoribine intermittent pulse protocol for induction therapy for systemic lupus erythematosus in children: an open-label pilot study with five newly diagnosed patients
  106. Treatment of difficult cases of systemic-onset juvenile idiopathic arthritis with tacrolimus
  107. Acute renal failure with encephalopathy following Salmonellaenteritidis infection
  108. Long-term mizoribine intermittent pulse therapy for young patients with flare of lupus nephritis
  109. Leukocytapheresis for the treatment of refractory systemic-onset juvenile idiopathic arthritis
  110. Renal Biopsy Findings in Children Receiving Long-Term Treatment with Cyclosporine A Given as a Single Daily Dose
  111. Low-dose cyclosporine A in a patient with X-linked immune dysregulation, polyendocrinopathy and enteropathy
  112. Implication of the peak serum level of mizoribine for control of the serum anti-dsDNA antibody titer in patients with lupus nephritis
  113. Single-dose daily administration of cyclosporin A for refractory nephrotic syndrome
  114. Mizoribine Pulse Therapy for a Pediatric Patient with Steroid-Resistant Nephrotic Syndrome
  115. Mizoribine for the treatment of lupus nephritis in children and adolescents
  116. Combined therapy of enalapril and losartan attenuates histologic progression in immunoglobulin A nephropathy
  117. Severe tubulointerstitial nephritis in a boy with refractory nephrotic syndrome
  118. Single-dose daily administration of cyclosporin�A for relapsing nephrotic syndrome
  119. Spontaneous remission of persistent severe hematuria in an adolescent with nutcracker syndrome: seven years? observation
  120. Repeat renal biopsy in children with severe idiopathic tubulointerstitial nephritis
  121. Effective Therapy of a Child Case of Refractory Nephrotic Syndrome with Tacrolimus
  122. Letter
  123. Mizoribine oral pulse therapy for patients with disease flare of lupus nephritis
  124. Successful treatment with leukocytapheresis in refractory Henoch-Sch�nlein purpura: case report
  125. Mizoribine oral pulse therapy for a patient with severe lupus nephritis
  126. Acute renal failure due to hypertension: Malignant hypertension in an adolescent
  127. End-Stage Kidney at the Onset of Nephrotic Syndrome in a 4-Year-Old Girl
  128. Childhood idiopathic membranous glomerulonephritis with isolated antinuclear antibody positivity
  129. Disseminated candidiasis following prednisolone therapy in systemic lupus erythematosus
  130. Rapidly progressive, pauci-immune diffuse crescentic glomerulonephritis in an infant
  131. Immunogenicity and Therapeutic Efficacy of Dendritic–Tumor Hybrid Cells Generated by Electrofusion
  132. Subsequent Progression to Membranous Glomerulonephritis Following Exacerbation of Urticarial Rash in Systemic Lupus Erythematosus: Report of 2 Cases.
  133. A Japanese Child with Senior-Loken Syndrome
  134. Repeat renal biopsy in a girl with tubulointerstitial nephritis and uveitis syndrome
  135. Methylprednisolone pulse therapy in Japanese children with severe lupus nephritis
  136. Senior-Loken syndrome associated with mental retardation and microcephaly
  137. Acute renal failure at the onset of idiopathic nephrotic syndrome in two children
  138. Thrombotic Stroke in a Child with Diarrhea-Associated Hemolytic-Uremic Syndrome with a Good Recovery.
  139. Tubulointerstitial Nephritis and Uveitis Syndrome in Two Siblings.
  140. Contribution of macromolecular IgA 1 to IgA abnormality in IgA nephropathy
  141. Interstitial cystitis and ileus in pediatric-onset systemic lupus erythematosus
  142. Allogeneic CD34-selected peripheral stem cell transplant for acute non-lymphocytic leukemia (FAB M5a) developed from juvenile chronic myelogenous leukemia
  143. A phase I dose escalation study of multicyclic, dose-intensive chemotherapy with peripheral blood stem cell support for small cell lung cancer
  144. Acute Glomerulonephritis Superimposed on Focal Segmental Glomerulosclerosis: A Case Report
  145. Complete Occulusion of Left Renal Artery in Pediatric-Onset Takayasu's Arteritis
  146. Focal Segmental Glomerulosclerosis: Unremitting Proteinuria of Long Duration as a Possible Etiology ?
  147. Distal type of renal tubular acidosis after anti-epileptic therapy in a girl with infantile spasms
  148. Acute glomerulonephritis associated with pneumonia: A possible Chlamydia pneumoniae etiology?
  149. Glomerulonephritis without IgA deposits in a case of Henoch-Schönlein purpura
  150. Acute Tubulointerstitial Nephritis Following Intravenous Immunoglobulin Therapy in a Male Infant with Minimal-Change Nephrotic Syndrome.
  151. Long-Term Azathioprine Therapy in Two Children with Steroid-Dependent Minimal-Change Nephrotic Syndrome.
  152. Subclinical Sjögren's syndrome: A significant67gallium accumulation in the orbits and parotid glands
  153. Trisomy 6 in a childhood acute mixed lineage leukemia
  154. An infant case of bilateral small kidneys with both proximal and distal tubular dysfunction
  155. Successful treatment of Wernicke's encephalopathy in a boy with acute mixed lineage leukemia
  156. Age-Related Histologic Alterations after Prednisolone Therapy in Children with IgA Nephropathy.
  157. Efficacy of Long-Term Sulfamethoxazole-Trimethoprim Therapy in a Boy with Hyperimmunoglobulin E Syndrome.
  158. Capacity of H2O2 Release from Monocytes in Steroid-Sensitive Nephrotic Sytndrome.
  159. Production of monocyte chemoattractant protein-1 by bovine glomerular endothelial cells