All Stories

  1. Genetic Screening of Patients With Inherited Fanconi Syndrome
  2. Recurrent C3 glomerulopathy after prolonged remission
  3. Toll‐Like Receptor 3 Activation in Lupus Nephritis: A Renal Signature Supporting “Pseudoviral” Immunity
  4. Unveiling long-standing low-molecular-weight proteinuria: A proximal tubular mitochondrial enzyme impairment caused by EHHADH mutation
  5. Tripartite motif 22 (TRIM22) downregulates TLR3-induced CCL5 expression in human renal proximal tubular epithelial cells
  6. Long‐term outcome of tacrolimus‐based immunosuppressive treatment for patients with paediatric‐onset lupus nephritis
  7. Recovery from rituximab-associated persistent hypogammaglobulinaemia in children with nephrotic syndrome
  8. Cylindromatosis lysine 63 deubiquitinase (CYLD) suppress TLR3-mediated CCL5 expression in human renal proximal tubular epithelial cells
  9. Interferon‐stimulated gene 56 positively regulates Toll‐like receptor 3‐mediated CXCL10 expression in human renal proximal tubular epithelial cells
  10. Early add-on use of belimumab as induction therapy for patients with childhood-onset systemic lupus erythematosus
  11. Clinical Characteristics of Cryopyrin‐Associated Periodic Syndrome and Long‐Term Real‐World Efficacy and Tolerability of Canakinumab in Japan: Results of a Nationwide Survey
  12. Be aware of severe juvenile chronic iridocyclitis without evidence of arthritis: Juvenile chronic iridocyclitis revisited
  13. Expression of interferon-stimulated gene 20 (ISG20), an antiviral effector protein, in glomerular endothelial cells: possible involvement of ISG20 in lupus nephritis
  14. Long-term outcome of tacrolimus monotherapy in a patient with lupus nephritis: A 12-year observation
  15. Glomerular endothelial expression of type I IFN-stimulated gene, DExD/H-Box helicase 60 via toll-like receptor 3 signaling: possible involvement in the pathogenesis of lupus nephritis
  16. Underrecognized Frasier syndrome revisited: Paradoxical immunocomplex deposition
  17. Be aware of underlying Dent disease in young boys with massive proteinuria
  18. Interleukin-6 via Toll-Like Receptor 3 Signaling Attenuates the Expression of Proinflammatory Chemokines in Human Podocytes
  19. Inhibitory effect of anti-malarial agents on the expression of proinflammatory chemokines via Toll-like receptor 3 signaling in human glomerular endothelial cells
  20. Podocyte sphingomyelin phosphodiesterase acid-like 3b decreases among children with idiopathic nephrotic syndrome
  21. Orthostatic proteinuria revisited: new clinical impact of the “old” clinical entity?
  22. Interferon-induced transmembrane protein 1 and Myxovirus resistance protein 1 are induced by polyinosinic-polycytidylic acid in cultured hCMEC/D3 human cerebral microvascular endothelial cells
  23. Endothelial expression of fractalkine (CX3CL1) is induced by Toll-like receptor 3 signaling in cultured human glomerular endothelial cells
  24. Complete clinical resolution of a Japanese family with renal pseudohypoaldosteronism type 1 due to a novel NR3C2 mutation
  25. High prevalence of underlying orthostatic proteinuria in young Japanese women
  26. Induction of C‐C motif chemokine ligand 2 through Toll‐like receptor 3 signaling in human cerebral microvascular endothelial cell/D3 cells: possible regulation by nuclear factor‐κB
  27. Fatal case of Hajdu-Cheney syndrome with idiopathic pulmonary hemosiderosis
  28. Cytosolic Sensors of Viral RNA Are Involved in the Production of Interleukin-6 via Toll-Like Receptor 3 Signaling in Human Glomerular Endothelial Cells
  29. Overweight Children at a Primary School in Hirosaki City: A Longitudinal, Individualized, Observational Study
  30. Interferon-stimulated gene 60 (ISG60) constitutes a negative feedback loop in the downstream of TLR3 signaling in hCMEC/D3 cells
  31. Chloroquine attenuates TLR3-mediated plasminogen activator inhibitor-1 expression in cultured human glomerular endothelial cells
  32. <b>Gnetin C suppresses double-stranded RNA-induced C-C motif chemokine ligand 2 (CCL2) and CCL5 production by inhibiting Toll-like receptor 3 signaling </b><b>pathway </b>
  33. Long-term clinicopathologic observation in a case of steroid-resistant nephrotic syndrome caused by a novel Crumbs homolog 2 mutation
  34. <b>Gnetin C, a resveratrol dimer, reduces amyloid-β 1–42 (Aβ42) production and ameliorates Aβ42-lowered cell viability in cultured SH-SY5Y human neuroblastoma </b><b>cells </b>
  35. Retinoic acid-inducible gene-I, melanoma differentiation-associated gene 5 and C-X-C motif chemokine ligand 10 are induced by a Toll-like receptor 3 agonist in human brain microvascular endothelial cells
  36. Toll-Like Receptor 3 Signaling Contributes to Regional Neutrophil Recruitment in Cultured Human Glomerular Endothelial Cells
  37. Free light chain-associated Fanconi syndrome in an adolescent
  38. Rebamipide reduces amyloid-β 1–42 (Aβ42) production and ameliorates Aβ43-lowered cell viability in cultured SH-SY5Y human neuroblastoma cells
  39. Urinary excretion of sphingomyelinase phosphodiesterase acid-like 3b in children with intractable nephrotic syndrome
  40. Expression of CCL5 is induced by polyinosinic : polycytidylic acid in cultured hCMEC/D3 human brain microvascular endothelial cells
  41. Treatment of pediatric-onset lupus nephritis: a proposal of optimal therapy
  42. Interferon (IFN)-induced protein 35 (IFI35) negatively regulates IFN-β-phosphorylated STAT1-RIG-I-CXCL10/CCL5 axis in U373MG astrocytoma cells treated with polyinosinic-polycytidylic acid
  43. Post-acute ischemic change and colon stricture in hemolytic uremic syndrome
  44. Chloroquine attenuates TLR3/IFN-β signaling in cultured normal human mesangial cells: A possible protective effect against renal damage in lupus nephritis
  45. Cylindromatosis (CYLD), a Deubiquitinase, Attenuates Inflammatory Signaling Pathways by Activating Toll-Like Receptor 3 in Human Mesangial Cells
  46. <b>DEC1 negatively regulates the expression of CXCL10 and CCL5 induced by poly IC in normal human mesangial </b><b>cells </b>
  47. Clarithromycin attenuates the expression of monocyte chemoattractant protein-1 by activating toll-like receptor 4 in human mesangial cells
  48. Hyper-IgE syndrome with a novel mutation of the STAT3 gene
  49. Does Dent disease remain an underrecognized cause for young boys with focal glomerulosclerosis?
  50. Monitoring of Epstein–Barr virus load and killer T cells in patients with juvenile idiopathic arthritis treated with methotrexate or tocilizumab
  51. Interferon-stimulated gene (ISG) 60, as well as ISG56 and ISG54, positively regulates TLR3/IFN-β/STAT1 axis in U373MG human astrocytoma cells
  52. Interferon (IFN)-Induced Protein 35 (IFI35), a Type I Interferon-Dependent Transcript, Upregulates Inflammatory Signaling Pathways by Activating Toll-Like Receptor 3 in Human Mesangial Cells
  53. Interferon-Stimulated Gene 15, a Type I Interferon-Dependent Transcript, Is Involved in a Negative Feedback Loop in Innate Immune Reactions in Human Mesangial Cells
  54. Expressions of mRNA for innate immunity-associated functional molecules in urinary sediment in immunoglobulin A nephropathy
  55. Carnosic acid attenuates apoptosis induced by amyloid-β 1–42 or 1–43 in SH-SY5Y human neuroblastoma cells
  56. Desferrioxamine, an iron chelator, inhibits CXCL10 expression induced by polyinosinic–polycytidylic acid in U373MG human astrocytoma cells
  57. Alteration in the podoplanin–ezrin–cytoskeleton linkage is an important initiation event of the podocyte injury in puromycin aminonucleoside nephropathy, a mimic of minimal change nephrotic syndrome
  58. Severe intrinsic acute kidney injury associated with therapeutic doses of acetaminophen
  59. Mizoribine in the treatment of pediatric-onset glomerular disease
  60. Toll-like receptor 3 signaling contributes to the expression of a neutrophil chemoattractant, CXCL1 in human mesangial cells
  61. ISG54 and ISG56 are induced by TLR3 signaling in U373MG human astrocytoma cells: Possible involvement in CXCL10 expression
  62. Efficacy of mizoribine-tacrolimus-based induction therapy for pediatric lupus nephritis
  63. Tumor necrosis factor-α synergistically enhances polyinosinic-polycytidylic acid-induced toll-like receptor 3 signaling in cultured normal human mesangial cells: possible involvement in the pathogenesis of lupus nephritis
  64. Carnosic acid suppresses the production of amyloid-β 1-42 and 1-43 by inducing an α-secretase TACE/ADAM17 in U373MG human astrocytoma cells
  65. Efficacy of long-term multidrug therapy in a patient with focal segmental glomerulosclerosis
  66. Mizoribine selectively attenuates monocyte chemoattractant protein-1 production in cultured human glomerular mesangial cell: A possible benefit of its use in the treatment of lupus nephritis
  67. Glomerular expression of myxovirus resistance protein 1 in human mesangial cells: Possible activation of innate immunity in the pathogenesis of lupus nephritis
  68. Single dose of rituximab for pediatric-onset refractory systemic lupus erythematosus
  69. Severe post-streptococcal acute glomerulonephritis and periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome
  70. Long-Term Tacrolimus-Based Immunosuppressive Treatment for Young Patients with Lupus Nephritis: A Prospective Study in Daily Clinical Practice
  71. Inflammatory Chemokine Expression via Toll-Like Receptor 3 Signaling in Normal Human Mesangial Cells
  72. Interaction between Interferon-Stimulated Gene 56 and Melanoma Differentiation-Associated Gene 5 in Toll-Like Receptor 3 Signaling in Normal Human Mesangial Cells
  73. TLR4 signaling induces retinoic acid-inducible gene-I and melanoma differentiation-associated gene 5 in mesangial cells
  74. Urinary Fractalkine and Monocyte Chemoattractant Protein-1 as Possible Predictors of Disease Activity of Childhood Glomerulonephritis
  75. A young girl with refractory intestinal Behçet’s disease: a case report and review of literatures on pediatric cases who received an anti-tumor necrosis factor agent
  76. Persistent Immature Glomeruli in a Girl with Refractory Nephrotic Syndrome
  77. Glomerular expression of fractalkine is induced by polyinosinic-polycytidylic acid in human mesangial cells: possible involvement of fractalkine after viral infection
  78. Long-term multidrug therapy in an adolescent patient with proliferative lupus nephritis: a trial of less cytotoxic therapy
  79. Treatment of young patients with lupus nephritis using calcineurin inhibitors
  80. Melanoma Differentiation-Associated Gene 5 Regulates the Expression of a Chemokine CXCL10 in Human Mesangial Cells: Implications for Chronic Inflammatory Renal Diseases
  81. Imbalance towards Th1 pathway predominance in purpura nephritis with proteinuria
  82. Autoantibodies to villin occur frequently in IPEX, a severe immune dysregulation, syndrome caused by mutation of FOXP3
  83. Polyinosinic-Polycytidylic Acid Induces the Expression of Interferon-Stimulated Gene 20 in Mesangial Cells
  84. Novel multidrug therapy for children with cyclosporine-resistant or -intolerant nephrotic syndrome
  85. Tacrolimus monotherapy in a patient with lupus flare using once-daily administration protocol
  86. Basic-helix-loop-helix transcription factor DEC2 constitutes negative feedback loop in IFN-β-mediated inflammatory responses in human mesangial cells
  87. Addition of mizoribine to the prednisolone plus tacrolimus treatment regimen in a patient with lupus flare
  88. Successful Multidrug Treatment of a Pediatric Patient with Severe Churg-Strauss Syndrome Refractory to Prednisolone
  89. Clinical responses to EGFR-tyrosine kinase inhibitor retreatment in non-small cell lung cancer patients who benefited from prior effective gefitinib therapy: a retrospective analysis
  90. Efficacy and safety of tacrolimus in 101 consecutive patients with rheumatoid arthritis: a possible alternative treatment to methotrexate?
  91. Retinoic acid-inducible gene-I is induced by double-stranded RNA and regulates the expression of CC chemokine ligand (CCL) 5 in human mesangial cells
  92. Mizoribine attenuates renal injury and macrophage infiltration in patients with severe lupus nephritis
  93. Potential Th1/Th2 predominance in children with newly diagnosed IgA nephropathy
  94. Intravenous immunoglobulin therapy leading to dramatic improvement in a patient with systemic juvenile idiopathic arthritis and severe pericarditis resistant to steroid pulse therapy
  95. Retinoic acid-inducible gene-I (RIG-I) is induced by IFN-  in human mesangial cells in culture: possible involvement of RIG-I in the inflammation in lupus nephritis
  96. Benefits of Once-Daily Administration of Cyclosporine A for Children with Steroid-Dependent, Relapsing Nephrotic Syndrome
  97. IFN-γ and TNF-α Synergistically Induce microRNA-155 Which Regulates TAB2/IP-10 Expression in Human Mesangial Cells
  98. Use of recombinant human serum albumin in pediatric patients with nephrotic syndrome
  99. A novel multidrug therapy for difficult cyclosporine-resistant focal segmental glomerulosclerosis
  100. Mizoribine Treatment of Young Patients with Severe Lupus Nephritis: A Clinicopathologic Study by the Tohoku Pediatric Study Group
  101. Vesical varices and telangiectasias in a patient with ataxia telangiectasia
  102. Effective treatment of young patients with pediatric-onset, long-standing lupus nephritis with tacrolimus given as a single daily dose: an open-label pilot study
  103. Long-term intermittent pulse therapy with mizoribine attenuates histologic progression in young patients with severe lupus nephritis: Report of two patients (Brief Communication)
  104. Mizoribine intermittent pulse protocol for induction therapy for systemic lupus erythematosus in children: an open-label pilot study with five newly diagnosed patients
  105. Treatment of difficult cases of systemic-onset juvenile idiopathic arthritis with tacrolimus
  106. Acute renal failure with encephalopathy following Salmonellaenteritidis infection
  107. Long-term mizoribine intermittent pulse therapy for young patients with flare of lupus nephritis
  108. Leukocytapheresis for the treatment of refractory systemic-onset juvenile idiopathic arthritis
  109. Renal Biopsy Findings in Children Receiving Long-Term Treatment with Cyclosporine A Given as a Single Daily Dose
  110. Low-dose cyclosporine A in a patient with X-linked immune dysregulation, polyendocrinopathy and enteropathy
  111. Implication of the peak serum level of mizoribine for control of the serum anti-dsDNA antibody titer in patients with lupus nephritis
  112. Single-dose daily administration of cyclosporin A for refractory nephrotic syndrome
  113. Mizoribine Pulse Therapy for a Pediatric Patient with Steroid-Resistant Nephrotic Syndrome
  114. Mizoribine for the treatment of lupus nephritis in children and adolescents
  115. Combined therapy of enalapril and losartan attenuates histologic progression in immunoglobulin A nephropathy
  116. Severe tubulointerstitial nephritis in a boy with refractory nephrotic syndrome
  117. Single-dose daily administration of cyclosporin�A for relapsing nephrotic syndrome
  118. Spontaneous remission of persistent severe hematuria in an adolescent with nutcracker syndrome: seven years? observation
  119. Repeat renal biopsy in children with severe idiopathic tubulointerstitial nephritis
  120. Effective Therapy of a Child Case of Refractory Nephrotic Syndrome with Tacrolimus
  121. Letter
  122. Mizoribine oral pulse therapy for patients with disease flare of lupus nephritis
  123. Successful treatment with leukocytapheresis in refractory Henoch-Sch�nlein purpura: case report
  124. Mizoribine oral pulse therapy for a patient with severe lupus nephritis
  125. Acute renal failure due to hypertension: Malignant hypertension in an adolescent
  126. End-Stage Kidney at the Onset of Nephrotic Syndrome in a 4-Year-Old Girl
  127. Childhood idiopathic membranous glomerulonephritis with isolated antinuclear antibody positivity
  128. Disseminated candidiasis following prednisolone therapy in systemic lupus erythematosus
  129. Rapidly progressive, pauci-immune diffuse crescentic glomerulonephritis in an infant
  130. Immunogenicity and Therapeutic Efficacy of Dendritic–Tumor Hybrid Cells Generated by Electrofusion
  131. Subsequent Progression to Membranous Glomerulonephritis Following Exacerbation of Urticarial Rash in Systemic Lupus Erythematosus: Report of 2 Cases.
  132. A Japanese Child with Senior-Loken Syndrome
  133. Repeat renal biopsy in a girl with tubulointerstitial nephritis and uveitis syndrome
  134. Methylprednisolone pulse therapy in Japanese children with severe lupus nephritis
  135. Senior-Loken syndrome associated with mental retardation and microcephaly
  136. Acute renal failure at the onset of idiopathic nephrotic syndrome in two children
  137. Thrombotic Stroke in a Child with Diarrhea-Associated Hemolytic-Uremic Syndrome with a Good Recovery.
  138. Tubulointerstitial Nephritis and Uveitis Syndrome in Two Siblings.
  139. Contribution of macromolecular IgA 1 to IgA abnormality in IgA nephropathy
  140. Interstitial cystitis and ileus in pediatric-onset systemic lupus erythematosus
  141. Allogeneic CD34-selected peripheral stem cell transplant for acute non-lymphocytic leukemia (FAB M5a) developed from juvenile chronic myelogenous leukemia
  142. A phase I dose escalation study of multicyclic, dose-intensive chemotherapy with peripheral blood stem cell support for small cell lung cancer
  143. Acute Glomerulonephritis Superimposed on Focal Segmental Glomerulosclerosis: A Case Report
  144. Complete Occulusion of Left Renal Artery in Pediatric-Onset Takayasu's Arteritis
  145. Focal Segmental Glomerulosclerosis: Unremitting Proteinuria of Long Duration as a Possible Etiology ?
  146. Distal type of renal tubular acidosis after anti-epileptic therapy in a girl with infantile spasms
  147. Acute glomerulonephritis associated with pneumonia: A possible Chlamydia pneumoniae etiology?
  148. Glomerulonephritis without IgA deposits in a case of Henoch-Schönlein purpura
  149. Acute Tubulointerstitial Nephritis Following Intravenous Immunoglobulin Therapy in a Male Infant with Minimal-Change Nephrotic Syndrome.
  150. Long-Term Azathioprine Therapy in Two Children with Steroid-Dependent Minimal-Change Nephrotic Syndrome.
  151. Subclinical Sjögren's syndrome: A significant67gallium accumulation in the orbits and parotid glands
  152. Trisomy 6 in a childhood acute mixed lineage leukemia
  153. An infant case of bilateral small kidneys with both proximal and distal tubular dysfunction
  154. Successful treatment of Wernicke's encephalopathy in a boy with acute mixed lineage leukemia
  155. Age-Related Histologic Alterations after Prednisolone Therapy in Children with IgA Nephropathy.
  156. Efficacy of Long-Term Sulfamethoxazole-Trimethoprim Therapy in a Boy with Hyperimmunoglobulin E Syndrome.
  157. Capacity of H2O2 Release from Monocytes in Steroid-Sensitive Nephrotic Sytndrome.
  158. Production of monocyte chemoattractant protein-1 by bovine glomerular endothelial cells